Lymphangioma - Limfangioma
Limfangioma (Lymphangioma) sò malformazioni di u sistema linfaticu carattarizati da lesioni chì sò cisti di pareti sottili. Sti malformazioni ponu accade à ogni età è ponu involucà ogni parte di u corpu, ma 90% si trovanu in i zitelli di menu di 2 anni di età è implicanu a testa è u collu. I linfangiomi sò comunmente diagnosticati prima di nascita cù ultrasonografia fetale. I linfangiomi acquistati ponu esse da traumu, inflammazioni o obstruczione linfatica. Siccomu ùn anu micca chance di diventà maligni, i linfangiomi sò generalmente trattati solu per ragioni cusmetichi.
☆ In i risultati Stiftung Warentest 2022 da Germania, a satisfaczione di i cunsumatori cù ModelDerm era solu ligeramente più bassu chè cù cunsultazioni di telemedicina pagate.
References
Lymphangioma hè ancu cunnisciutu com'è malformazione linfatica (LM) . Hè un disordine vascular presente da a nascita. Hè carattarizatu da a crescita anormali di u tissutu linfaticu prima è dopu à a nascita. Lymphangioma affetta circa 1 in 2000 à 4000 persone, senza differenza significativa trà i sessi o razzi. A maiò parte di i casi (80-90%) sò diagnosticati prima di dui anni. I sintomi varienu assai, da l'inflamazione localizzata à l'anormalità estensiva in i canali linfatici, à volte chì portanu à un inzuccheru severu cunnisciutu com'è elefantiasis. Per esempiu, lymphangioma in u collu è a faccia pò causà gonfiore faciale, è in casi severi, disfigurement. Quandu affetta a lingua, pò purtà à a crescita di a mandibula è i denti misalignati. In a bocca è u collu, pò causà prublemi di respirazione è emergenze per a vita. In l'ochji, pò causà a perdita di vista, u muvimentu limitatu di l'ochji, e palpebre cadenti, è l'occhi sbulicati. L'implicazione di i membri pò causà gonfiore è crescita anormali di tessuti è osse. Stu tumore di solitu cresce lentamente, ma infizzioni, cambiamenti hormonali, o ferite pò causà un rapidu crescita, chì ponenu risichi per a vita chì necessitanu trattamentu urgente.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
In questu studiu retrospettivu, avemu rivista 24 zitelli chì avianu lymphangioma è sò stati trattati cù injections di suluzione bleomicina da ghjennaghju 1999 à dicembre 2004. A maiò parte di e ferite (63%) si n'andò completamente, u 21% hà avutu una bona risposta, è u 16% ùn hà micca rispostu bè. Dui pazienti anu tornatu u tumore dopu, è dui altri anu avutu l'abscessi induve anu avutu l'iniezioni. Per furtuna, ùn avemu micca vistu altri grandi prublemi o effetti secundari.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
I tipi principali di lymphangioma sò i seguenti - lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Questi custituiscenu circa 26% di i tumori vascular benigni in i zitelli, ma sò menu cumuni in l'adulti. Lymphangioma circumscriptum , u tipu più frequente, mostra i dutti linfatichi chì sporgenu da a pelle, furmendu vesiculi chiari pieni di fluidu simili à a spawn di rana, inseme cù gonfiore di i tessuti. Tipicamenti appare nantu à e zoni cù una ricca reta linfatica cum'è i membri, u troncu è l'ascelle. Una donna di 71 anni hè ghjunta à a nostra clinica cù gonfiore persistente di a gamba, bumps rosati nantu à i genitali, prurito è perdite di fluidu linfaticu. On a supprimé chirurgicalement toutes les bosses grâce à une procédure appelée labiectomie majeure bilatérale, en s'arrêtant à l'échelle du fascia de Colles, tout en conservant le clitoris et la fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
