Lymphangioma - Linfangioma
Los Linfangioma (Lymphangioma) son malformaciones del sistema linfático caracterizadas por lesiones que son quistes de paredes delgadas. Estas malformaciones pueden ocurrir a cualquier edad y pueden afectar cualquier parte del cuerpo, pero el 90% ocurren en niños menores de 2 años y afectan la cabeza y el cuello. Los linfangiomas comúnmente se diagnostican antes del nacimiento mediante ecografía fetal. Los linfangiomas adquiridos pueden ser el resultado de un traumatismo, inflamación u obstrucción linfática. Dado que no tienen posibilidades de volverse malignos, los linfangiomas generalmente se tratan únicamente por razones estéticas.
☆ En los resultados de 2022 del Stiftung Warentest de Alemania, la satisfacción del consumidor con ModelDerm fue sólo ligeramente inferior que con las consultas de telemedicina pagadas.
References
Lymphangioma también se conoce como malformación linfática (LM) . Es un trastorno vascular presente desde el nacimiento. Se caracteriza por un crecimiento anormal de tejido linfático antes y después del nacimiento. Lymphangioma afecta aproximadamente a 1 de cada 2000 a 4000 personas, sin diferencias significativas entre géneros o razas. La mayoría de los casos (80 a 90%) se diagnostican antes de los dos años. Los síntomas varían ampliamente, desde hinchazón localizada hasta anomalías extensas en los canales linfáticos, que a veces conducen a una hinchazón grave conocida como elefantiasis. Por ejemplo, lymphangioma en el cuello y la cara puede provocar hinchazón facial y, en casos graves, desfiguración. Cuando afecta la lengua, puede provocar un crecimiento excesivo de la mandíbula y dientes desalineados. En la boca y el cuello, puede causar problemas respiratorios y emergencias potencialmente mortales. En los ojos, puede causar pérdida de visión, movimiento ocular limitado, párpados caídos y ojos saltones. La afectación de las extremidades puede causar hinchazón y crecimiento anormal de tejidos y huesos. Este tumor generalmente crece lentamente, pero las infecciones, los cambios hormonales o las lesiones pueden provocar un crecimiento rápido, lo que plantea riesgos potencialmente mortales que requieren tratamiento urgente.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
En este estudio retrospectivo, revisamos a 24 niños que tenían lymphangioma y fueron tratados con inyecciones de solución de bleomicina desde enero de 1999 hasta diciembre de 2004. La mayoría de las lesiones (63%) desaparecieron por completo, el 21% obtuvo una buena respuesta y el 16% no respondió bien. A dos pacientes les volvió el tumor más tarde y a otros dos les salieron abscesos en el lugar donde recibieron las inyecciones. Afortunadamente, no vimos ningún otro problema importante ni efectos secundarios.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
Los principales tipos de lymphangioma son los siguientes: lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Representan alrededor del 26% de los tumores vasculares benignos en niños, pero son menos comunes en adultos. Lymphangioma circumscriptum , el tipo más frecuente, muestra conductos linfáticos que sobresalen a través de la piel, formando vesículas llenas de líquido transparente similares a las huevas de rana, junto con inflamación del tejido. Suele aparecer en zonas con una rica red linfática como las extremidades, el tronco y las axilas. Una mujer de 71 años acudió a nuestra clínica con hinchazón persistente en las piernas, bultos rosados en los genitales, picazón y pérdida de líquido linfático. Eliminamos quirúrgicamente todos los bultos con un procedimiento llamado labiectomía mayor bilateral, deteniéndonos en el nivel de la fascia de Colles, preservando al mismo tiempo el clítoris y la horquilla.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
