Juvenile xanthogranuloma - Jeugd Xanthogranulomahttps://en.wikipedia.org/wiki/Juvenile_xanthogranuloma
☆ Yn 'e 2022 Stiftung Warentest-resultaten út Dútslân wie de konsuminttefredenheid mei ModelDerm mar wat leger dan mei betelle telemedisynkonsultaasjes. It is karakteristyk om in bytsje giel uterlik te hawwen.
Giele nodule by bern. Typysk Jeugd Xanthogranuloma (Juvenile xanthogranuloma)
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References Juvenile Xanthogranuloma 30252359 NIH
Juvenile xanthogranuloma (JXG) is in frij gewoane tastân en it meast foarkommende type non-Langerhans cell histiocytic disorder by bern. Yn sa'n 75% fan 'e gefallen ferskine dizze lesions binnen it earste jier fan it libben, en mear as 15-20% fan pasjinten hawwe se fan berte ôf. Wylst seldsum yn folwoeksenen, JXG typysk komt meast faak yn minsken yn harren lette tweintich oant tritich, en de measte folwoeksen pasjinten hawwe mar ien lesion. Klinysk ferskynt it as inkele of meardere giel-oranje-brune stevige bulten of bulten, benammen op it gesicht, nekke en boppeliif. Orale lesions binne ûngewoan, mar kinne ferskine as in giele knobbel oan 'e kanten fan' e tonge of earne oars yn 'e mûle, mooglik liedend ta zweren en bloeden. Hûdlesjes feroarsaakje normaal gjin symptomen en tendearje oer ferskate jierren op har eigen te gean. Hoewol seldsum, is okulêre belutsenens it meast foarkommende probleem bûten de hûd, folge troch longûntwikkeling. Ocular JXG beynfloedet gewoanlik mar ien each en komt foar yn minder dan 0. 5 % fan pasjinten, hoewol sawat 40% fan dyjingen mei okulêre belutsenheid ek meardere hûdlesjes hawwe as se diagnostearre binne.
Juvenile xanthogranuloma (JXG) is a relatively common entity and is the most common form of non-Langerhans cell histiocytic disorder of childhood., It is estimated that in 75% of cases, lesions appear during the first year of life, with >15-20% of patients having lesions at birth. JXG is rare in adults, with a peak incidence in the late twenties to thirties. The majority of adult patients have solitary lesions. Typically, the clinical presentation consists of solitary or multiple yellow-orange-brown firm papules or nodules. The most common locations are the face, neck, and upper torso. Oral lesions are rare and often occur as a yellow nodule on the lateral aspects of the tongue. Oral lesions can also arise on the gingival, buccal mucosa, and midline hard palate and may ulcerate and bleed. Cutaneous lesions are usually asymptomatic, and most lesions spontaneously involute over the course of several years. Although occurring rarely, ocular involvement is the most common extracutaneous site involved, followed by the lungs. Ocular JXG is nearly always unilateral and develops in less than 0.5% of patients. Approximately 40% of patients with ocular JXG, however, have multiple cutaneous lesions at the time of diagnosis.
Juvenile Xanthogranuloma: An Entity With a Wide Clinical Spectrum 32721389Juvenile xanthogranulomas (JXGs) binne ûngewoane, goedaardige sykten dy't diel útmeitsje fan in gruttere kategory fan non-Langerhans cell histiocytoses. Se ferskine typysk as ien of mear reade of giele bulten, faak fûn op 'e holle of hals. De measte JXG's ûntwikkelje by berte of binnen it earste jier fan it libben. Hoewol it ûngewoan is, kinne se soms gebieten bûten de hûd beynfloedzje, wêrby't belutsenheid fan 'e eagen wat is om nei te sjen neffens besteande literatuer. Yn 't algemien geane JXG's op' e hûd op harsels fuort en hawwe typysk gjin behanneling nedich.
Juvenile xanthogranulomas (JXGs) are uncommon, benign diseases that are part of a larger category of non-Langerhans cell histiocytoses. They typically show up as one or more red or yellowish lumps, often found on the head or neck. Most JXGs develop either at birth or within the first year of life. While it's unusual, sometimes they can affect areas beyond the skin, with eye involvement being something to watch for according to existing literature. Generally, JXGs on the skin go away on their own and typically don't need treatment.
Okulêre lesion manifestearret yn oant 10% fan minsken mei JXG en kin har fisy beynfloedzje. Hoewol't kutane lesions meastentiids spontaan ferdwine, okulêre lesions ferbetterje selden spontaan en fereaskje behanneling.