Lymphangioma
Lymphangioma binne misfoarmingen fan it lymfesysteem, karakterisearre troch lesions dy't tinne muorre cysten binne. Dizze misfoarmingen kinne op elke leeftyd foarkomme en kinne elk diel fan it lichem belûke, mar 90% komme foar yn bern ûnder 2 jier en belûke de holle en nekke. Ferwurven lymphangiomas kinne resultearje út trauma, ûntstekking, of lymfatyske obstruksje. Om't se gjin kâns hawwe om maligne te wurden, wurde lymfangioma's gewoanlik allinich behannele foar kosmetyske redenen.
☆ Yn 'e 2022 Stiftung Warentest-resultaten út Dútslân wie de konsuminttefredenheid mei ModelDerm mar wat leger dan mei betelle telemedisynkonsultaasjes.
References
Lymphangioma is ek bekend as lymfatyske malformation (LM) . It is in vaskulêre oandwaning oanwêzich fan berte. It is karakterisearre troch abnormale groei fan lymfeweefsel foar en nei berte. Lymphangioma hat ynfloed op sawat 1 op 2000 oant 4000 minsken, sûnder signifikant ferskil tusken geslachten of rassen. De measte gefallen (80-90%) wurde diagnostearre foar leeftyd twa. Symptomen fariearje breed, fan pleatslike swelling oant wiidweidige abnormaliteiten yn 'e lymfekanalen, soms liedend ta slimme swelling bekend as elefantiasis. Bygelyks, lymphangioma yn 'e nekke en gesicht kin swelling fan it gesicht feroarsaakje, en yn slimme gefallen, misfoarming. As it beynfloedet de tonge, kin it liede ta kaak oergroei en misaligned tosken. Yn 'e mûle en nekke kin it sykheljenproblemen en libbensbedrige needgevallen feroarsaakje. Yn 'e eagen kin it fisyferlies feroarsaakje, beheinde eachbeweging, hingjende oogleden en bulte eagen. Limb belutsenens kin swelling en abnormale groei fan weefsels en bonken feroarsaakje. Dizze tumor groeit normaal stadich, mar ynfeksjes, hormonale wizigingen of blessueres kinne rappe groei feroarsaakje, libbensbedrige risiko's dy't urgent behanneling nedich binne.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Yn dizze retrospektive stúdzje hawwe wy 24 bern besjoen dy't lymphangioma hiene en waarden behannele mei ynjeksjes fan bleomycin-oplossing fan jannewaris 1999 oant desimber 2004. De measte fan 'e lesions (63%) gongen folslein fuort, 21% krige in goede reaksje, en 16% reagearre net goed. Twa pasjinten hiene de tumor letter weromkaam, en twa oaren krigen absesjes wêr't se de ynjeksjes krigen. Gelokkich seagen wy gjin oare grutte problemen of side-effekten.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
De haadtypen fan lymphangioma binne as folget - lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Dizze foarmje sawat 26% fan goedaardige vaskulêre tumors yn bern, mar binne minder faak by folwoeksenen. Lymphangioma circumscriptum , it meast foarkommende type, toant lymfekanalen dy't troch de hûd útstekke, en foarmje dúdlike floeistoffolle vesikels lykas kikkertspawn, tegearre mei weefselswelling. It ferskynt typysk op gebieten mei in ryk lymfatyske netwurk lykas de ledematen, romp en oksels. In 71-jierrige frou kaam nei ús klinyk mei oanhâldende skonkswelling, rôze bulten op har geslachtsdielen, jeuk en lekkende lymfefluid. Wy hawwe alle bulten sjirurgysk fuorthelle mei in proseduere neamd bilaterale grutte labiectomy, stoppe op Colles 'fascia-nivo, wylst de klitoris en fourchette behâlde.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
