Lymphangioma
https://en.wikipedia.org/wiki/Lymphangioma
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References
Recent Progress in Lymphangioma 34976885 NIH
Tugtar anchúram limfach (LM) ar Lymphangioma freisin. Is neamhord congénach é atá i láthair ó bhreith. Tá sé tréithrithe mar fás neamhghnách ar fhiúcháin limfacha roimh agus tar éis breithe. Tá Lymphangioma i dtrácht ar thart ar 1 i 2000 go 4000 duine, gan aon difríocht shuntasach idir inscne nó cin. Déantar diagnóis i bhformhór na gcásanna (80‑90 %) roimh dhá bhliain d’aois. Athraíonn na comharthaí go forleathan, ó swelláil áitiúil go máiníméideanna difríocha ionsaitheacha i gcnáill limfacha, rud a fhágann go mbíonn sé dainséarach, le eilifintiasis uaireanta. Mar shampla, is féidir le lymphangioma sa mhúinéal agus ar an aghaidh a bheith ina chúis le swelláil aghaidhe, agus i gcásanna dainséarach, mí-chumadh. Nuair a chuireann sé isteach ar an teanga, is féidir go gcuirfidh sé le forfhás an ghoil agus le fiacla mífhhoirfe. Sa bhéal agus sa mhúinéal, féadann sé fadhbanna análaithe agus éigeandálaí a bheith bagrach don bheatha. Sna súile, d’fhéadfadh sé a bheith ina chúis le caillteanas radharc, gluaiseacht súl teoranta, ptosis (drochiú na seolta), agus exophthalmos (súile bulga). Is féidir le baint ghéag a bheith ina chúis le swelláil nó gíogantais, le fás neamhghnách na fhiúchan agus na cnámh. Fásann an meall seo go mall de ghnáth, ach féadann ionfhabhtuithe, athruithe hormónacha, nó gortú fás tapa a spreagadh, rud a chruthaíonn rioscaí a bhfuil bagairt mhór ar an mbeatha agus a éilíonn cóireáil práinneach láithreach.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma: Is intralesional bleomycin sclerotherapy effective? 22279495 NIH
Sa staidéar siarbhunaithe seo, rinneamar athbhreithniú ar 24 leanbh a raibh lymphangioma acu agus a fuair cóireáil le innéacs isteach le bleomycin uisceach ó Eanáir 1999 go Nollaig 2004. D'éirigh le réiteach iomlán i 63 % (15/24) de na lesaí, fuair 21 % freagra maith, agus 16 % níor fuair freagra maith. Athfhill an gairm i 2 othar. Fuair beirt eile cruthú absais ag an áit innéacsála. Níor mothaíodh aon chúraimí tromchúiseacha eile ná aon éifeachtaí fo-iarmhairí eile.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
Surgical Resection of Acquired Vulvar Lymphangioma Circumscriptum - Case reports 24665431 NIH
Seo a leanas na príomhchineálacha lymphangioma – lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Ionann iad seo agus thart ar 26 % de thumóirí fásaigh neamhurchóideacha i leanaí ach níl siad chomh coitianta i measc daoine fásta. Léiríonn lymphangioma circumscriptum, an cineál is coitianta, dúchtaí limfeacha ar an bharrfhóiréigin tríd an epiderma, ag cruthú clúdaigh soiléire líonta le leacht cosúil le sceith frog, agus éadain comhcheangailte. De ghnáth bíonn sé le feiceáil ar an gcrúca dlíog, ar an tronc, agus ar an axilla, a bhfuil córas limfatach saibhir ann. Tháinig bean 71 bliain d’aois chuig ár gclínic le edéime leanúnach ar a chos íseal, clúdaigh bándearg ar a baill íseal, pruritus, agus leacht limfatach le sceitheadh. Bhaineamar na clúdaigh go léir go máinliachta trí mhórlabiectomy déthaobhach, ag gearradh síos go leibhéal fása Colles, agus ag caomhnú an clítiris agus an ceathairéad.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.