Tha Neurofibroma na thumar neoni-rùisgte anns an t-siostam nearbhach iomaill. Ann an 90% de chùisean, lorgar iad mar tumors leotha fhèin gun eas-òrdugh ginteil sam bith. Ach, lorgar an còrr ann an daoine le neurofibromatosis seòrsa I (NF1), galar a tha air a shealbhachadh gu ginteil le autosomal. Faodaidh iad raon de chomharran a thoirt gu buil bho mhì-dhealbhadh corporra agus pian gu ciorram inntinneil.
Faodaidh neurofibroma a bhith eadar 2 agus 20 mm ann an trast-thomhas, tha e bog, flaccid, agus pinc-geal. Faodar biopsy a chleachdadh airson breithneachadh histopathology.
Mar as trice bidh neurofibroma ag èirigh anns na deugairean agus gu tric bidh iad às deidh breith-bhreith. Ann an daoine le Neurofibromatosis Seòrsa I, tha iad buailteach leantainn air adhart a’ dol am meud ann an àireamh agus meud fhad ‘s a tha iad nan inbheach.
A neurofibroma is a benign nerve-sheath tumor in the peripheral nervous system. In 90% of cases, they are found as stand-alone tumors, while the remainder are found in persons with neurofibromatosis type I (NF1), an autosomal-dominant genetically inherited disease. They can result in a range of symptoms from physical disfiguration and pain to cognitive disability.
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Neurofibroma den euslainteach le neurofibromatosis.
Tha neurofibromas buailteach a dhol nas miosa le aois. Nochd na leòintean anns an neach seo an toiseach nuair a bha e na dheugaire.
Tha Neurofibromas nan tumhan neo-àbhaisteach cumanta a lorgar ann an nerves iomaill. Mar as trice bidh iad coltach ri cnapan bog air a’ chraiceann no cnapan beaga fodha. Bidh iad a’ fàs bhon endoneurium agus na figheagan ceangail timcheall air sguaban nerve iomallach. Neurofibromas are the most prevalent benign peripheral nerve sheath tumor. Often appearing as a soft, skin-colored papule or small subcutaneous nodule, they arise from endoneurium and the connective tissues of peripheral nerve sheaths.
Faodaidh neurofibroma a bhith eadar 2 agus 20 mm ann an trast-thomhas, tha e bog, flaccid, agus pinc-geal. Faodar biopsy a chleachdadh airson breithneachadh histopathology.
Mar as trice bidh neurofibroma ag èirigh anns na deugairean agus gu tric bidh iad às deidh breith-bhreith. Ann an daoine le Neurofibromatosis Seòrsa I, tha iad buailteach leantainn air adhart a’ dol am meud ann an àireamh agus meud fhad ‘s a tha iad nan inbheach.