Lymphangioma - Linfangioma
Linfangioma (Lymphangioma) son malformacións do sistema linfático caracterizadas por lesións que son quistes de paredes finas. Estas malformacións poden ocorrer a calquera idade e poden afectar a calquera parte do corpo, pero o 90% ocorren en nenos menores de 2 anos e afectan a cabeza e o pescozo. Os linfanxiomas son comunmente diagnosticados antes do nacemento mediante ecografía fetal. Os linfangiomas adquiridos poden resultar de trauma, inflamación ou obstrución linfática. Dado que non teñen posibilidades de converterse en malignos, os linfangiomas adoitan tratarse só por motivos estéticos.
☆ Nos resultados de Stiftung Warentest de Alemaña de 2022, a satisfacción dos consumidores con ModelDerm foi só lixeiramente inferior á das consultas de telemedicina pagas.
References
Lymphangioma tamén se coñece como malformación linfática (LM) . É un trastorno vascular presente dende o nacemento. Caracterízase por un crecemento anormal do tecido linfático antes e despois do nacemento. Lymphangioma afecta aproximadamente a 1 de cada 2000 a 4000 persoas, sen diferenzas significativas entre xéneros ou razas. A maioría dos casos (80-90%) diagnostícanse antes dos dous anos. Os síntomas varían moito, desde inchazo localizado ata anomalías extensas nas canles linfáticas, que ás veces provocan inchazo grave coñecido como elefantiasis. Por exemplo, lymphangioma no pescozo e na cara pode causar inchazo facial e, en casos graves, desfiguración. Cando afecta a lingua, pode provocar un crecemento excesivo da mandíbula e dentes desalineados. Na boca e no pescozo, pode causar problemas respiratorios e emerxencias que ameazan a vida. Nos ollos, pode causar perda de visión, movemento ocular limitado, pálpebras caídas e ollos saltones. A afectación das extremidades pode causar inchazo e crecemento anormal de tecidos e ósos. Este tumor adoita crecer lentamente, pero as infeccións, os cambios hormonais ou as lesións poden provocar un crecemento rápido, poñendo en perigo a vida e que requiren tratamento urxente.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Neste estudo retrospectivo, revisamos 24 nenos que tiñan lymphangioma e foron tratados con inxeccións de solución de bleomicina desde xaneiro de 1999 ata decembro de 2004. A maioría das lesións (63%) desapareceron por completo, o 21% obtivo unha boa resposta e o 16% non respondeu ben. A dous pacientes volveu o tumor máis tarde, e outros dous tiveron abscesos onde recibiron as inxeccións. Afortunadamente, non vimos ningún outro gran problema ou efectos secundarios.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
Os principais tipos de lymphangioma son os seguintes: lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Estes representan ao redor do 26% dos tumores vasculares benignos en nenos, pero son menos frecuentes nos adultos. Lymphangioma circumscriptum , o tipo máis frecuente, amosa condutos linfáticos que sobresaen pola pel, formando vesículas claras cheas de líquido semellantes á posta de ras, xunto cunha inflamación dos tecidos. Normalmente aparece en áreas cunha rica rede linfática como os membros, o tronco e as axilas. Unha muller de 71 anos acudiu á nosa clínica con inchazo persistente das pernas, protuberancias rosadas nos xenitais, comezón e fuga de líquido linfático. Eliminamos cirurxicamente todas as protuberancias cun procedemento chamado labiectomía maior bilateral, parando a nivel da fascia de Colles, conservando o clítoris e o fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
