Juvenile xanthogranuloma
https://en.wikipedia.org/wiki/Juvenile_xanthogranuloma
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Nodule rawaya a cikin yara. Na al'ada Juvenile xanthogranuloma
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References
Juvenile Xanthogranuloma 30252359 NIH
Juvenile xanthogranuloma (JXG) cuta ce da ta zama ruwan dare gama gari kuma galibi nau'in non-Langerhans cell histiocytic disorder a yara. A cikin kusan 75% na lokuta, waɗannan raunuka suna nunawa a cikin farkon shekara ta rayuwa, kuma fiye da 15-20% na marasa lafiya suna da su daga haihuwa. Duk da yake ba kasafai ba a cikin manya, JXG yawanci yana faruwa mafi sau da yawa a cikin mutane a ƙarshen shekaru ashirin zuwa talatin, kuma yawancin marasa lafiya na manya suna da rauni ɗaya kawai. A asibiti, yana bayyana kamar guda ɗaya ko ma yawa rawaya-orange-launin ruwan kasa mai ƙarfi ko dunƙulewa, galibi akan fuska, wuya, da na sama. Raunin baka ba sabon abu bane amma yana iya fitowa a matsayin dunƙule rawaya a gefen harshe ko kuma wani wuri a cikin baki, mai yiwuwa ya haifar da ulcers da zub da jini. Raunin fata yawanci ba sa haifar da bayyanar cututtuka kuma yakan tafi da kansu sama da shekaru da yawa. Ko da yake ba kasafai ba, shigar ido shine batun da ya fi kowa fiye da fata, sannan shigar huhu ya biyo baya. Ocular JXG yawanci yana shafar ido ɗaya ne kawai kuma yana faruwa a ƙasa da 0. 5 % na marasa lafiya, kodayake kusan kashi 40% na waɗanda ke da sa hannun ido kuma suna da raunuka da yawa idan an gano su.
Juvenile xanthogranuloma (JXG) is a relatively common entity and is the most common form of non-Langerhans cell histiocytic disorder of childhood., It is estimated that in 75% of cases, lesions appear during the first year of life, with >15-20% of patients having lesions at birth. JXG is rare in adults, with a peak incidence in the late twenties to thirties. The majority of adult patients have solitary lesions. Typically, the clinical presentation consists of solitary or multiple yellow-orange-brown firm papules or nodules. The most common locations are the face, neck, and upper torso. Oral lesions are rare and often occur as a yellow nodule on the lateral aspects of the tongue. Oral lesions can also arise on the gingival, buccal mucosa, and midline hard palate and may ulcerate and bleed. Cutaneous lesions are usually asymptomatic, and most lesions spontaneously involute over the course of several years. Although occurring rarely, ocular involvement is the most common extracutaneous site involved, followed by the lungs. Ocular JXG is nearly always unilateral and develops in less than 0.5% of patients. Approximately 40% of patients with ocular JXG, however, have multiple cutaneous lesions at the time of diagnosis.
Juvenile Xanthogranuloma: An Entity With a Wide Clinical Spectrum 32721389Juvenile xanthogranulomas (JXGs) cuta ce da ba a saba gani ba, waɗanda ke cikin babban nau'in non-Langerhans cell histiocytoses. Yawanci suna nunawa kamar guda ɗaya ko fiye ja ko rawaya, galibi ana samun su a kai ko wuya. Yawancin JXGs suna tasowa ko dai a lokacin haihuwa ko a cikin shekarar farko ta rayuwa. Duk da yake yana da sabon abu, wani lokacin suna iya shafar wuraren da suka wuce fata, tare da shigar da ido ya zama abin dubawa bisa ga adabin da ake da su. Gabaɗaya, JXGs akan fata suna tafi da kansu kuma yawanci basa buƙatar magani.
Juvenile xanthogranulomas (JXGs) are uncommon, benign diseases that are part of a larger category of non-Langerhans cell histiocytoses. They typically show up as one or more red or yellowish lumps, often found on the head or neck. Most JXGs develop either at birth or within the first year of life. While it's unusual, sometimes they can affect areas beyond the skin, with eye involvement being something to watch for according to existing literature. Generally, JXGs on the skin go away on their own and typically don't need treatment.
Raunin ido yana bayyana har zuwa 10% na mutanen da ke da JXG kuma yana iya shafar hangen nesa. Ko da yake raunukan fata suna ɓacewa ba zato ba tsammani, raunin ido da wuya ya inganta ba da daɗewa ba kuma yana buƙatar magani.