Urticaria pigmentosa - Urtikè Pigmentosa
Urtikè Pigmentosa (Urticaria pigmentosa) se fòm ki pi komen nan mastositoz kutane. Li se yon maladi ra ki te koze pa kantite twòp nan mast selil nan po a ki pwodui itikè oswa blesi sou po a lè irite. Tach wouj oswa mawon yo souvan wè sou po a, tipikman alantou pwatrin lan, fwon, ak do. Selil mast sa yo, lè yo irite (pa egzanp lè w fwote po a, ekspoze chalè), pwodui twòp histamine, sa ki lakòz yon reyaksyon alèjik ki mennen nan itikè ki lokalize nan zòn iritasyon an, pafwa yo rele "siy Darier la".
☆ Nan rezilta Stiftung Warentest 2022 ki soti nan Almay, satisfaksyon konsomatè yo ak ModelDerm te sèlman yon ti kras pi ba pase ak konsiltasyon telemedsin peye.
References
Mastocytosis se yon kondisyon kote gen yon eksè de selil mast, souvan yo jwenn nan divès pati nan kò tankou po a, mwèl zo a, ak sistèm dijestif. Dapre Òganizasyon Mondyal Lasante (OMS) , cutaneous mastocytosis ka klase nan twa kalite prensipal. Premye kalite a (mastocytomas) konsiste de blesi solitè oswa kèk (≤3) . Dezyèm kalite a (urticaria pigmentosa) enplike blesi miltip, tipikman sòti nan plis pase 10 a mwens pase 100. Dènye kalite a montre patisipasyon toupatou atravè po a. Urticaria pigmentosa se fòm ki pi komen nan mastositoz kutane nan timoun, men li ka rive tou nan granmoun. Anjeneral se yon kondisyon inofansif ki souvan amelyore pandan adolesans. Kontrèman ak mastositoz granmoun, urticaria pigmentosa raman afekte ògàn entèn yo. Youn nan karakteristik diferan nan urticaria pigmentosa se tandans li yo lakòz ti, grate, tach wouj-mawon oswa jòn-mawon oswa blesi sou po a, souvan ke yo rekonèt kòm itikè. Tach sa yo anjeneral parèt nan anfans epi yo ka dire pandan tout lavi.
Mastocytosis is a disorder characterized by mast cell accumulation, commonly in the skin, bone marrow, gastrointestinal (GI) tract, liver, spleen, and lymphatic tissues. The World Health Organization (WHO) divides cutaneous mastocytosis into 3 main presentations. The first has solitary or few (≤3) lesions called mastocytomas. The second, urticaria pigmentosa (UP), involves multiple lesions ranging from >10 to <100 lesions. The last presentation involves diffuse cutaneous involvement. UP is the most common cutaneous mastocytosis in children, but it can form in adults as well. It is considered a benign, self-resolving condition that often remits in adolescence. Unlike adult forms of mastocytosis, there is rarely any internal organ involvement in UP. What makes UP particularly distinctive is its tendency to manifest as small, itchy, reddish-brown, or yellowish-brown spots or lesions on the skin, commonly referred to as urticaria or hives. These spots typically appear in childhood and can persist throughout a person's life.
Mastocytosis is a disorder characterized by mast cell accumulation, commonly in the skin, bone marrow, gastrointestinal (GI) tract, liver, spleen, and lymphatic tissues. The World Health Organization (WHO) divides cutaneous mastocytosis into 3 main presentations. The first has solitary or few (≤3) lesions called mastocytomas. The second, urticaria pigmentosa (UP), involves multiple lesions ranging from >10 to <100 lesions. The last presentation involves diffuse cutaneous involvement. UP is the most common cutaneous mastocytosis in children, but it can form in adults as well. It is considered a benign, self-resolving condition that often remits in adolescence. Unlike adult forms of mastocytosis, there is rarely any internal organ involvement in UP. What makes UP particularly distinctive is its tendency to manifest as small, itchy, reddish-brown, or yellowish-brown spots or lesions on the skin, commonly referred to as urticaria or hives. These spots typically appear in childhood and can persist throughout a person's life.
Yon ti fi 6-zan te vini ak plizyè tach ki gen koulè nwa ki te parèt premye sou po tèt li epi li te gaye nan figi l ak kò l pandan sis mwa ki sot pase yo. Li mansyone santi yo leve, vin wouj, ak grate lè yo te aplike presyon. Li pa t 'fè eksperyans bouj, vomisman, dyare, oswa souf anlè, epi istwa medikal pèsonèl li ak fanmi li pa te bay endikasyon ki enpòtan. Apre egzamen an, nou te jwenn plizyè tach nwa sou po tèt li, fwon, figi, ak kou li, ansanm ak tach nwa yon ti kras leve sou pwatrin li ak do li. Lejèman fwote tach yo te lakòz yo anfle ak demanjezon nan 2 minit, men sentòm yo disparèt nan 15-20 minit (Darier's sign) .
A 6-year-old female, presented with multiple dark-colored lesions, which started over the scalp and further progressed to involve the face and trunk since past six months. She gave a history of elevation, redness, and itching on the lesions on application of pressure. There was no associated flushing, vomiting, diarrhoea, or wheeze. The personal and family history was not contributory. On examination, there were multiple hyperpigmented macules over the scalp, forehead, face, and neck in addition to minimally elevated hyperpigmented plaques over the chest and the back. Gentle rubbing of the lesions elicited urtication and itching within 2 min and it resolved within 15–20 minutes, suggestive of the Darier's sign.
A 6-year-old female, presented with multiple dark-colored lesions, which started over the scalp and further progressed to involve the face and trunk since past six months. She gave a history of elevation, redness, and itching on the lesions on application of pressure. There was no associated flushing, vomiting, diarrhoea, or wheeze. The personal and family history was not contributory. On examination, there were multiple hyperpigmented macules over the scalp, forehead, face, and neck in addition to minimally elevated hyperpigmented plaques over the chest and the back. Gentle rubbing of the lesions elicited urtication and itching within 2 min and it resolved within 15–20 minutes, suggestive of the Darier's sign.
