Pityriasis lichenoides et varioliformis acuta (PLEVA) is a disease of the immune system. It is the more severe version of pityriasis lichenoides chronica. The disease is characterized by rashes and small lesions on the skin.
ミュシャ・ハーバーマン病としても知られる Pityriasis lichenoides et varioliformis acuta (PLEVA) は、鱗状の斑点のある赤茶色の発疹を引き起こすまれな皮膚疾患です。丘疹は進行して水疱、膿疱、潰瘍を形成する場合があり、これらの病変はかゆみや灼熱感を伴うことがあります。かゆみや灼熱感を感じることがよくあります。 PLEVA は通常、体幹、上腕、脚、特に皮膚のひだに影響を与えます。発疹は時間の経過とともに現れたり消えたりし、場合によっては何年も続きます。 Pityriasis lichenoides et varioliformis acuta (PLEVA), also known as Mucha-Habermann disease, is an uncommon cutaneous inflammatory rash characterized by diffuse red-brown papules in various stages with a mica-like scale on more established lesions. The papules may progress to form vesicles, pustules, and ulcers, and these lesions can be associated with pruritus or a burning sensation. PLEVA favors the trunk and proximal extremities, especially in the flexural regions. This rash tends to relapse and remit with variable duration, sometimes lasting up to years.