Lymphangioma - Limfangioma
Limfangioma (Lymphangioma) minangka malformasi sistem limfatik sing ditandai dening lesi kista kanthi dinding tipis. Malformasi iki bisa kedadeyan ing umur apa wae lan bisa mengaruhi bagian awak apa pun, nanging 90 % kedadeyan ing bocah sing umure kurang saka 2 taun lan paling asring ana ing sirah lan gulu. Limfangioma umume didiagnosis sadurunge lair nganggo ultrasonografi janin. Limfangioma sing muncul bisa disebabake trauma, inflamasi, utawa obstruksi limfatik. Amarga ora ana potensi dadi ganas, limfangioma biasane diobati mung kanggo alasan kosmetik.
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ReferencesLymphangioma uga dikenal minangka malformasi limfatik (LM). Iki minangka kelainan pembuluh darah sing ana wiwit lair. Iki ditondoi kanthi pertumbuhan jaringan limfatik sing ora normal sadurunge lan sawise lair. Lymphangioma kena pengaruh kira‑kira 1 ing 2000 nganti 4000 wong, ora ana bedane sing signifikan antarane jender utawa ras. Umume kasus (80‑90 %) didiagnosis sadurunge umur rong taun. Gejalaé béda‑bèda, saka pembengkakan lokal nganti abnormalitas ekstensif ing saluran limfatik, kadhangkala nyebabake pembengkakan parah sing dikenal minangka elephantiasis. Contone, lymphangioma ing gulu lan pasuryan bisa nyebabake pembengkakan rai, lan ing kasus sing abot, cacat. Nalika kena ing ilat, bisa nyebabake rahang tuwuh lan untu sing ora cocog. Ing tutuk lan gulu, bisa nyebabake masalah ambegan lan kahanan darurat sing ngancam nyawa. Ing mripat, bisa nyebabake kelangan penglihatan, gerakan mripat sing winates, kelopak mata sing mlorot, lan mripat sing mlengkung. Keterlibatan anggota awak bisa nyebabake pembengkakan lan pertumbuhan jaringan lan balung sing ora normal. Tumor iki biasane tuwuh alon‑alon, nanging infeksi, owah‑owahan hormonal, utawa ciloko bisa nyebabake pertumbuhan kanthi cepet, nambah risiko sing ngancam nyawa lan mbutuhake perawatan cepet.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Ing panaliten retrospektif iki, kita nliti 24 bocah sing duwe lymphangioma lan diobati kanthi injeksi larutan bleomycin wiwit Januari 1999 nganti Desember 2004. Lesi ilang ing 63% kasus, 21% entuk respon sing apik, lan 16% ora nanggapi kanthi apik. Loro pasien ngalami tumor bali mengko, lan loro liyane ngalami abses ing panggonan injeksi. Untunge, ora ana masalah serius utawa efek samping liyane sing diamati.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
Jinis utama lymphangioma antara liya yaiku lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lan lymphangioendothelioma. Kelompok iki nyumbang kira‑kira 26 % saka tumor pembuluh darah jinak pada anak‑anak, nanging jarang ditemui pada orang dewasa. Lymphangioma circumscriptum, jenis yang paling umum, menampilkan saluran limfatik yang menonjol pada kulit, membentuk vesikel berisi cairan jernih seperti kodok, disertai pembengkakan jaringan di sekitarnya. Biasanya muncul pada area dengan jaringan limfatik yang melimpah, seperti anggota tubuh, batang tubuh, dan ketiak. Seorang wanita berusia 71 tahun datang ke klinik kami dengan pembengkakan kaki yang persisten, benjolan pada kelamin, gatal, serta cairan limfa yang keluar. Kami mengangkat seluruh benjolan dengan prosedur yang disebut labiektomi mayor bilateral, berhenti pada tingkat fascia Colles, sambil mempertahankan klitoris dan fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
