Neurofibroma yaiku tumor jinak saka selubung saraf ing sistem saraf perifer. Ing 90 % kasus, tumor iki ditemokake minangka lesi mandiri tanpa kelainan genetik. Nanging, ing sisa kasus ditemokake ing wong sing duwe neurofibromatosis tipe I (NF1), penyakit warisan autosomal dominan. Kondisi iki bisa nyebabake macem‑macem gejala, saka cacat fisik lan nyeri nganti gangguan kognitif.
Neurofibroma bisa duwe diameter 2 nganti 20 mm, alus, lentur, lan werna putih jambon. Biopsi bisa digunakake kanggo diagnosa histopatologi.
Neurofibroma biasane muncul ing masa remaja lan asring sawise pubertas. Ing wong sing duwe Neurofibromatosis Tipe I, lesi iki cenderung terus nambah jumlah lan ukuran nalika diwasa.
A neurofibroma is a benign nerve-sheath tumor in the peripheral nervous system. In 90% of cases, they are found as stand-alone tumors, while the remainder are found in persons with neurofibromatosis type I (NF1), an autosomal-dominant genetically inherited disease. They can result in a range of symptoms from physical disfiguration and pain to cognitive disability.
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Neurofibroma saka pasien sing kena neurofibromatosis.
Neurofibromas cenderung nambah bareng nambahé umur. Lesi ing individu iki pisanan muncul nalika dheweke isih enom.
Neurofibromas minangka tumor jinak sing umum ditemokake ing saraf perifer. Biasane katon kaya benjolan alus ing kulit utawa benjolan cilik ing ngisor kulit. Tumor iki berkembang saka endoneurium lan jaringan ikat ing sakupenge sarung saraf perifer. Neurofibromas are the most prevalent benign peripheral nerve sheath tumor. Often appearing as a soft, skin-colored papule or small subcutaneous nodule, they arise from endoneurium and the connective tissues of peripheral nerve sheaths.
Neurofibroma bisa duwe diameter 2 nganti 20 mm, alus, lentur, lan werna putih jambon. Biopsi bisa digunakake kanggo diagnosa histopatologi.
Neurofibroma biasane muncul ing masa remaja lan asring sawise pubertas. Ing wong sing duwe Neurofibromatosis Tipe I, lesi iki cenderung terus nambah jumlah lan ukuran nalika diwasa.