Lymphangioma
https://en.wikipedia.org/wiki/Lymphangioma
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References
Recent Progress in Lymphangioma 34976885 NIH
Lymphangioma wekî malformasyona lîmfatîk (LM) jî tê zanîn. Ew nexweşiyek damarî ye ku ji zayînê ve heye. Ew bi mezinbûna anormal ya tevna lîmfatîk berî û piştî zayînê tê diyar kirin. Lymphangioma li ser 1 ji 2000 heta 4000 kesan bandor dike, bêyî ku cûdahiyek girîng di navbera zayend an nijadan de tune. Piraniya bûyeran (% 80-90) beriya du salî têne teşhîs kirin. Nîşan pir cûda dibin, ji werimîna herêmî bigire heya anormaliyên berfireh ên di kanalên lîmfê de, carinan dibe sedema werimîna giran ku wekî elephantiasis tê zanîn. Mînakî, lymphangioma di stû û rû de dikare bibe sedema werimîna rû, û di rewşên giran de, şikestin. Dema ku ew bandorê li ser ziman dike, ew dikare bibe sedema mezinbûna çeneyê û diranên xelet. Di dev û stûyê de, ew dikare bibe sedema pirsgirêkên nefesê û acîlên xeternak ên jiyanê. Di çavan de, dibe ku bibe sedema windabûna dîtinê, tevgera çavê sînordar, ketina çavan, û geşbûna çavan. Tevlêbûna lingan dikare bibe sedema werimandin û mezinbûna anormal ya tevn û hestiyan. Ev tumor bi gelemperî hêdî mezin dibe, lê enfeksiyon, guhertinên hormonal, an birîndar dibe sedema mezinbûna bilez, xetereyên xeternak ên jiyanê ku hewceyê dermankirina lezgîn e.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma: Is intralesional bleomycin sclerotherapy effective? 22279495 NIH
Di vê lêkolîna paşverû de, me 24 zarokên ku lymphangioma hebûn û bi derziyên çareseriya bleomycinê ji Çile 1999 heta Kanûn 2004 hatin derman kirin, lêkolîn kir. Piraniya birînan (63%) bi tevahî çûn, 21% bersivek baş stend, û 16% baş bersiv neda. Li du nexweşan tûmor paşê vegeriya, û du kesên din jî li cihê ku derzî lê kirin abscess ketin. Xwezî, me tu pirsgirêk û bandorên alîgir ên din nedît.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
Surgical Resection of Acquired Vulvar Lymphangioma Circumscriptum - Case reports 24665431 NIH
Cûreyên sereke yên lymphangioma wiha ne - lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Vana derdora 26% ji tumorên damar ên benignî di zarokan de pêk tînin lê di mezinan de kêmtir in. Lymphangioma circumscriptum , cureya herî pir caran, rêyên lîmfatîk ên ku di nav çerm de derdikevin, nîşan dide, vezîkulên dagirtî yên zelal ên mîna şitila beqan, ligel werimîna tevnvîsê çê dikin. Ew bi gelemperî li deverên xwedan torgilokek lîmfatîk a dewlemend ên mîna ling, stûn û milan xuya dike. Jineke 71 salî bi werimîna lingên xwe yên domdar, gemarên pembe yên li ser organên wê yên genîtal, xiş û şînahiya lîmfê hat klînîka me. Me bi neştergerî bi pêvajoyek ku jê re labiektomiya mezin a dualî tê gotin, li ser asta fascia ya Colles sekinîn, di heman demê de klîtoris û fourchette parastin.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.