Lymphangiomahttps://en.wikipedia.org/wiki/Lymphangioma
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References Recent Progress in Lymphangioma 34976885 NIH
Lymphangioma Notum est etiam ac malformation lymphatica (LM) . Vascularis perturbatio est a nativitate praesens. Abnormis incrementum textus lymphatici ante et post partum notatur. Lymphangioma afficit circiter 1 in 2000 ad 4000 hominum, nulla significativa differentia inter genera vel gentes. Pleraque (80-90%) praecogniti sunt ante duos annos. Symptomata late variant a tumore locali ad abnormitates in lymphaticis canalibus latis, interdum ad tumorem gravem quae elephantiasim notae. Verbi gratia, lymphangioma in collo et facie potest tumorem facialem, in gravibus casibus deformem facere. Cum linguam afficit, potest ducere ad excrescentias maxillares et dentes misalignos. In ore et collo, difficultates spirandi et vitae minaces casus causare potest. In oculis, potest facere visum damnum, oculus motus limitatus, palpebrae demissa, et oculi tumes. Ingressio membrorum tumorem et abnormes incrementum textuum et ossium causare potest. Hic tumor tardius crescit, at infectiones, mutationes hormonales, vel iniuria incrementum celeritatis causare possunt, pericula vitae minaces ponendi quae urgentem curationem requirunt.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma: Is intralesional bleomycin sclerotherapy effective? 22279495 NIH
In hoc studio retrospectivo recensuimus 24 haedos qui lymphangioma habebant et injectiones solutionis bleomycinum a Ianuario MCMXCIX ad Decembrem 2004 tractavimus. Pleraque laesionum (63%) perfecte discesserunt, 21% bonam responsionem acceperunt et 16% non bene respondere. Duobus serius aegris tumor, alii duo abscessibus, ubi injectiones ceperunt. Feliciter alias magnas difficultates vel effectus latus non vidimus.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
Surgical Resection of Acquired Vulvar Lymphangioma Circumscriptum - Case reports 24665431 NIH
Genera lymphangioma principalia sunt haec - lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Hae circa 26% tubercula benigna in pueris constituunt, sed in adultis minus communia sunt. Lymphangioma circumscriptum , Typus frequentissimus, ductus lymphatici per cutem prominentes ostendit, liquido repleto vesiculas similes ranae parientis formans, cum texti tumore. Plerumque in areis apparet cum retis lymphaticis opulentis sicut membra, truncus et alis. A LXXI annorum femina ad nostram clinicam pervicit tumor cruris perseverans, rosea labefecit in genitalibus eius, pruritu, et fluido lymphatico stillante. Omnes labeculas surgically removimus cum processu labiectomy bilateralis majoris vocato, morando in gradu Colles' fasciae, servato clitoris et fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.