Lymphangioma - Lymphangiom
Lymphangiom (Lymphangioma) sinn Malformatiounen vum Lymphsystem, charakteriséiert duerch Läsionen, déi dënnwandeg Zysten sinn. Dës Fehlformatiounen kënnen zu all Alter optrieden an all Deel vum Kierper involvéieren, awer 90 % kommen bei Kanner ënner 2 Joer al an betreffen de Kapp an den Hals. Acquired Lymphangiome kënnen aus Trauma, Entzündung oder lymphatescher Obstruktioun entstoen. Well se keng Chance hunn, bösart ze ginn, ginn Lymphangiome normalerweis nëmmen aus kosmeteschen Grënn behandelt.
☆ AI Dermatology — Free Service
An den 2022 Stiftung Warentest Resultater aus Däitschland war d'Zefriddenheet vum Konsument mam ModelDerm nëmme liicht manner wéi mat bezuelte Telemedizin Konsultatiounen.
An den 2022 Stiftung Warentest Resultater aus Däitschland war d'Zefriddenheet vum Konsument mam ModelDerm nëmme liicht manner wéi mat bezuelte Telemedizin Konsultatiounen.
relevance score : -100.0%
ReferencesLymphangioma ass och bekannt als lymphatesch Malformatioun (LM). Et ass eng vaskulär Stéierung, déi vu Gebuert un d'Présenz huet. Et ass charakteriséiert duerch anormales Wuesstem vum Lymphgewebe virun an no der Gebuert. Lymphangioma beaflosst ongeféier 1 vun 2000 bis 4000 Leit, ouni wesentlechen Ënnerscheed tëscht Geschlechter oder Rassen. Déi meescht Fäll (80‑90 %) ginn virum Zweetzéngteralter diagnostizéiert. Symptomer variéieren vu lokaliséierter Schwellung bis zu extensiven Anomalien an de Lymphkanäl, heiansdo féieren zu schwéier Schwellungen, bekannt als Elephantiasis. Zum Beispill kann e Lymphangioma am Hals a Gesiicht Gesiichtsschwellungen verursaachen an an schwéiere Fäll zu Verformungen féieren. Wann et d'Zong beaflosst, kann et zu Kieferiwwerwuessen an falsch ausgeriichte Zänn féieren. Am Mond‑ a Halsberäich kann et Atmungsproblemer a liewensgeféierlech Noutfäll verursaachen. An den Aen kann et Visionsverloscht, limitéiert Aenbeweegungen, hängend Lidder an opbléissend Aen verursaachen. Limb Engagement kann Schwellungen an anormale Wuesstem vu Stoffer an de Schanken verursaachen. Dësen Tumor wiisst normalerweis lues, awer Infektiounen, hormonell Verännerungen oder Verletzungen kënnen e séier Wuesstem verursaachen, wat liewensgeféierlech Risiken matt, déi dréngend Behandlung erfuerderen.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
An dëser retrospektiver Studie hu mir 24 Kanner iwwerschaut, déi Lymphangioma haten a vun Januar 1999 bis Dezember 2004 mat Injektiounen vun Bleomycin‑Léisung behandelt goufen. D’méiwscht vun de Läsionen (63 %) sinn komplett fortgaang, 21 % kruten eng gutt Äntwert an 16 % hu net gutt reagéiert. Zwee Patientë kruten de Tumor méi spéit zréck, an zwee anerer kruten Abscesse, wou se d'Injektiounen kruten. Glécklecherweis hu mir keng aner grouss Problemer oder Nebenwirkungen gesinn.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
D'Haaptarten vun Lymphangioma sinn wéi follegt: Lymphangioma circumscriptum, cavernous Lymphangioma, cystic Hygroma, Lymphangioendothelioma. Dës stellen ongeféier 26 % vun de benigne vaskuläre Tumoren bei Kanner dar, awer si sinn manner heefeg bei Erwuessenen. Lymphangioma circumscriptum, déi heefegst Aart, weist lymphatesch Kanaelen, déi duerch d'Haut erausstinn, an bildet kloer, flësseg gefëllt Vesikelen, déi ähnlech wéi Frog Spawn ausgesinn, zesumme mat Gewebeschwellung. Et erschéngt typesch op Gebidder mat engem räiche Lymphnetz, wéi d'Gliederen, de Stamm an d'Achsel. Eng 71 Joer al Fra koum an eis Klinik mat persistenter Been‑Schwellung, rosa Knollen op hir Genitalien, Jucken an Lymphflëssegkeet. Mir hunn chirurgesch all d'Bumpen ewechgeholl mat enger Prozedur, déi bilateral grouss Labiectomie genannt gëtt, op dem Niveau vun der Colles‑Fascia gestoppt, wärend de Klitoris an d'Fourchette behaalt bleiwen.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
