Lymphangioma - Lymphangiom
Lymphangiom (Lymphangioma) sinn Malformatiounen vum Lymphsystem, charakteriséiert duerch Läsionen déi dënnwandeg Zysten sinn. Dës Fehlformatiounen kënnen zu all Alter optrieden a kënnen all Deel vum Kierper involvéieren, awer 90% kommen bei Kanner ënner 2 Joer al a betrëfft de Kapp an den Hals. Acquired Lymphangiome kënnen aus Trauma, Entzündung oder Lymphatesch Obstruktioun entstoen. Well se keng Chance hunn bösarteg ze ginn, ginn Lymphangiome normalerweis nëmme fir kosmetesch Grënn behandelt.
☆ An den 2022 Stiftung Warentest Resultater aus Däitschland war d'Zefriddenheet vum Konsument mam ModelDerm nëmme liicht manner wéi mat bezuelte Telemedizin Konsultatiounen.
References
Lymphangioma ass och bekannt als lymphatesch Malformatioun (LM) . Et ass eng vaskulär Stéierung präsent vun der Gebuert. Et ass charakteriséiert duerch anormal Wuesstum vum Lymphgewebe virun an no der Gebuert. Lymphangioma beaflosst ongeféier 1 an 2000 bis 4000 Leit, ouni wesentlechen Ënnerscheed tëscht Geschlechter oder Rennen. Déi meescht Fäll (80-90%) ginn virum Alter zwee diagnostizéiert. Symptomer variéiere wäit, vu lokaliséierter Schwellung bis extensiv Anomalie an de Lymphkanälen, heiansdo féiert zu schwéieren Schwellungen bekannt als Elephantiasis. Zum Beispill, lymphangioma am Hals a Gesiicht kann Gesiicht Schwellung verursaachen, an a schwéiere Fäll, Verformung. Wann et d'Zong beaflosst, kann et zu Kiefer Iwwerwuessen a falsch ausgeriicht Zänn féieren. Am Mond an Hals kann et Atmungsproblemer a liewensgeféierlech Noutfäll verursaachen. An den Ae kann et Visiounsverloscht verursaachen, limitéiert Aenbewegung, drooping eyelids, a bulging Aen. Limb Engagement kann Schwellung an anormal Wuesstum vu Stoffer a Schanken verursaachen. Dësen Tumor wächst normalerweis lues, awer Infektiounen, hormonell Verännerungen oder Verletzung kënnen e schnelle Wuesstum verursaachen, liewensgeféierlech Risiken, déi dréngend Behandlung erfuerderen.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
An dëser Retrospektiv Studie hu mir 24 Kanner iwwerpréift, déi lymphangioma haten a mat Injektiounen vu Bleomycin Léisung vu Januar 1999 bis Dezember 2004 behandelt goufen. Déi meescht vun de Läsionen (63%) sinn komplett fortgaang, 21% kruten eng gutt Äntwert an 16%. Huet net gutt reagéiert. Zwee Patiente kruten den Tumor méi spéit zréck, an zwee anerer kruten Abscesse wou se d'Injektiounen kruten. Glécklecherweis hu mir keng aner grouss Probleemer oder Nebenwirkungen gesinn.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
D'Haaptarten vun lymphangioma sinn wéi follegt - lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Dës maachen ongeféier 26% vu benigne vaskuläre Tumoren bei Kanner aus, awer si manner heefeg bei Erwuessener. Lymphangioma circumscriptum , déi heefegst Aart, weist lymphatesch Kanäl déi duerch d'Haut erausstinn, a bilden kloer flësseg gefëllte Vesikelen ähnlech wéi Frog Spawn, zesumme mat Tissue Schwellung. Et erschéngt typesch op Gebidder mat engem räiche Lymphnetz wéi d'Glieder, de Stamm an d'Achsel. Eng 71 Joer al Fra koum an eis Klinik mat persistent Been Schwellung, rosa Knollen op hir Genitalie, Jucken a Lymphflëssegkeet. Mir hu chirurgesch all d'Bumpen ewechgeholl mat enger Prozedur déi bilateral grouss Labiectomie genannt gëtt, op Colles Fascia Niveau gestoppt, wärend de Klitoris a Fourchette behalen.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
