Angiofibroma
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2022 m. Stiftung Warentest iš Vokietijos rezultatai rodo, kad vartotojų pasitenkinimas ModelDerm buvo tik šiek tiek mažesnis nei mokamų nuotolinės medicinos konsultacijų.
2022 m. Stiftung Warentest iš Vokietijos rezultatai rodo, kad vartotojų pasitenkinimas ModelDerm buvo tik šiek tiek mažesnis nei mokamų nuotolinės medicinos konsultacijų.
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ReferencesCutaneous angiofibromas gali atsirasti įvairiose kūno vietose. Ant veido jie dažnai vadinami pluoštinėmis papulėmis arba riebaline adenoma; ant varpos – pearly penile papules; po nagais – periungualinėmis angiofibromomis arba Koeneno navikais; o burnoje – burnos fibromomis. Veido angiofibromos yra ryškus tuberous sclerosis (TS) – paveldimo sutrikimo, pažeidžiančio odą, inkstus, širdį, smegenis ir plaučius, požymis. Paprastai jos atsiranda veido odoje vaikystėje arba ankstyvojoje pilname amžiuje asmenims, sergantiems TS. Trijų ar daugiau veido angiofibromų arba dviejų ar daugiau periungualinių angiofibromų buvimas yra reikšmingas diagnozuojant TS. Be to, esant sąlygoms, tokioms kaip multiple endocrine neoplasia type 1 (MEN-1) ir Birt‑Hogg‑Dubé syndrome, gali pasireikšti kelios veido angiofibromos. Pearly penile papules randamos palei vainikinį kraštą ir varpos galą. Tai patvarūs, neskausmingi iškilimai, dažniau pastebimi neapipjaustytiems vyrams.
Cutaneous angiofibromas can be located on different areas of the body including the face where they are commonly called fibrous papules or adenoma sebaceum on the penis where they are called pearly penile papules, underneath the nail where they are called periungual angiofibromas or Koenen tumors, and in the mouth where they are called oral fibromas. Facial angiofibromas are considered one of the most obvious clinical presentations of tuberous sclerosis (TS), an autosomal dominant hamartomatous disorder that affects the skin, kidneys, heart, brain, and lungs. With TS, angiofibromas typically arise on the face in childhood and early adulthood. Both facial angiofibromas (greater than or equal to 3 needed) and periungual angiofibroma (greater than or equal to 2 needed) are 2 of the major criteria for TS. Multiple facial angiofibromas are also found in multiple endocrine neoplasia type 1 (MEN-1) and Birt-Hogg-Dube syndrome. Pearly penile papules are chronic, asymptomatic, papules found on the coronal margin and sulcus of the penis. They are more common in uncircumcised men.
Cutaneous angiofibromas can be located on different areas of the body including the face where they are commonly called fibrous papules or adenoma sebaceum on the penis where they are called pearly penile papules, underneath the nail where they are called periungual angiofibromas or Koenen tumors, and in the mouth where they are called oral fibromas. Facial angiofibromas are considered one of the most obvious clinical presentations of tuberous sclerosis (TS), an autosomal dominant hamartomatous disorder that affects the skin, kidneys, heart, brain, and lungs. With TS, angiofibromas typically arise on the face in childhood and early adulthood. Both facial angiofibromas (greater than or equal to 3 needed) and periungual angiofibroma (greater than or equal to 2 needed) are 2 of the major criteria for TS. Multiple facial angiofibromas are also found in multiple endocrine neoplasia type 1 (MEN-1) and Birt-Hogg-Dube syndrome. Pearly penile papules are chronic, asymptomatic, papules found on the coronal margin and sulcus of the penis. They are more common in uncircumcised men.
1) veidas – Fibrous papule
2) varpos – Pearly penile papule
3) po rankų ar kojų nagų – Periungual angiofibroma