Lymphangioma
Lymphangioma dia fikorontanan'ny rafitry ny lymphatic izay misy ratra izay kista manify misy rindrina. Mety hitranga amin'ny sokajin-taona rehetra ireo tsy fahampiana ireo ary mety ho tafiditra amin'ny faritra rehetra amin'ny vatana, fa ny 90% dia mitranga amin'ny zaza latsaky ny 2 taona ary misy ny loha sy ny tendany. Ny lymphangioma dia matetika voan'ny aretina alohan'ny nahaterahana amin'ny fampiasana ultrasound foetal. Ny lymphangioma azo dia mety ho vokatry ny trauma, ny areti-maso, na ny fanakanana ny lymphatika. Satria tsy manana vintana ho lasa masiaka izy ireo, ny lymphangioma dia matetika tsaboina noho ny antony kosmetika fotsiny.
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References
Lymphangioma dia fantatra ihany koa amin'ny hoe malformation lymphatique (LM) . Fikorontanan'ny lalan-drà misy hatrany am-bohoka izany. Izy io dia miavaka amin'ny fitomboan'ny tavy lymphatika mialoha sy aorian'ny fiterahana. Lymphangioma dia misy fiantraikany eo amin'ny 1 amin'ny olona 2000 ka hatramin'ny 4000, tsy misy fahasamihafana lehibe eo amin'ny lahy sy ny vavy na ny firazanana. Ny ankamaroan'ny tranga (80-90%) dia voamarina alohan'ny roa taona. Miovaova be ny soritr'aretina, manomboka amin'ny fivontosana eo an-toerana ka hatramin'ny tsy fetezana be dia be ao amin'ny fantsona lymphatika, indraindray mitarika fivontosana mahery vaika antsoina hoe elefantiasis. Ohatra, ny lymphangioma ao amin'ny tendany sy ny tarehy dia mety hiteraka fivontosan'ny tarehy, ary amin'ny toe-javatra mafy dia mety ho kilemaina. Rehefa misy fiantraikany amin'ny lela izany, dia mety hitarika amin'ny fitomboan'ny valanorano sy ny nify diso. Ao amin'ny vava sy ny tendany dia mety hiteraka olana amin'ny fofonaina sy hamehana mahafaty. Eo amin'ny maso dia mety hiteraka fahaverezan'ny fahitana izany, voafetra ny fihetsehan'ny maso, ny hodi-maso mianjera ary ny maso mibontsina. Ny fidiran'ny rantsambatana dia mety miteraka fivontosana sy fitomboan'ny taolana sy taolana tsy ara-dalàna. Matetika io fivontosana io dia mitombo miadana, fa ny aretina, ny fiovan'ny hormona, na ny ratra dia mety hiteraka fitomboana haingana, ka miteraka risika mahafaty izay mitaky fitsaboana maika.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Tao anatin'ity fandalinana miverimberina ity, dia nandinika ankizy 24 izahay izay nanana lymphangioma ary notsaboina tamin'ny tsindrona vahaolana bleomycin nanomboka tamin'ny Janoary 1999 ka hatramin'ny Desambra 2004. Niala tanteraka ny ankamaroan'ny ratra (63%) , 21% nahazo valiny tsara, ary 16% tsy namaly tsara. Nisy marary roa niverina avy eo ilay fivontosana, ary nisy roa hafa voan'ny abscesses izay nahazoany tsindrona. Soa ihany fa tsy nahita olana lehibe hafa na voka-dratsy hafa izahay.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
Ny karazana lymphangioma dia toy izao manaraka izao - lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Manodidina ny 26 isan-jaton'ny fivontosana vascular malemy amin'ny ankizy ireo fa tsy fahita firy amin'ny olon-dehibe. Lymphangioma circumscriptum , ny karazana matetika indrindra, dia mampiseho lakandrano lymphatika mipoitra amin'ny hoditra, mamorona vesicles feno ranon-javatra mazava mitovy amin'ny fanatodizan'ny sahona, miaraka amin'ny fivontosan'ny sela. Matetika izy io no miseho amin'ny faritra misy tambajotra lymphatic manankarena toy ny rantsambatana, vatan-kazo ary armpits. Nisy vehivavy 71 taona tonga teny amin’ny toeram-pitsaboanay, ary nisy fivontosana tsy an-kijanona, fivontosana mavokely teo amin’ny fivaviany, mangidihidy, ary ranon’ny lymph mitete. Nesorinay tamin'ny fandidiana ny fivontosan'ny taolana rehetra tamin'ny fomba antsoina hoe labiectomy lehibe bilateral, mijanona amin'ny haavon'ny fascia Colles, ary mitahiry ny clitoris sy ny fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
