Angiofibroma
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relevance score : -100.0%
ReferencesCutaneous angiofibromas ka puta ki nga wahanga o te tinana. I te kanohi, he maha nga wa e mohiotia ana he fibrous papules (fibrous papule), adenoma sebaceum ranei; i te ure, ka kiia ko pearly penile papules; i raro i te whao, ka kiia ko periungual angiofibroma, ko Koenen tumors ranei; i roto i te waha, e kiia ana he oral fibromas (oral fibroma). Ko te angiofibroma kanohi he ahua nui o tuberous sclerosis (TS), he mate tuku iho e pa ana ki te kiri, ki ngā whatukuhu, ki te ngakau, ki te roro, ki ngā ngongo. I te nuinga o te wā ka tupu i runga i te kanohi i te wā o te tamarikitanga, i te wā o te pakeketanga o te hunga takitahi me te TS. Ko te toru, neke atu rānei ngā angiofibroma kanohi, e rua, neke atu rānei ngā angiofibroma periungual e kiia ana he mea nui ki te whakatau i te TS. I tua atu, he maha ngā angiofibroma kanohi kei roto i ngā ahuatanga (multiple endocrine neoplasia type 1 (MEN‑1) me Birt‑Hogg‑Dube syndrome). Pearly penile papules (pearly penile papules) kei te korona margin me te sulcus o te ure. He papules roa, kore mamae e kitea ana i ngā tāne kāore i te whakakotahi i te ure.
Cutaneous angiofibromas can be located on different areas of the body including the face where they are commonly called fibrous papules or adenoma sebaceum on the penis where they are called pearly penile papules, underneath the nail where they are called periungual angiofibromas or Koenen tumors, and in the mouth where they are called oral fibromas. Facial angiofibromas are considered one of the most obvious clinical presentations of tuberous sclerosis (TS), an autosomal dominant hamartomatous disorder that affects the skin, kidneys, heart, brain, and lungs. With TS, angiofibromas typically arise on the face in childhood and early adulthood. Both facial angiofibromas (greater than or equal to 3 needed) and periungual angiofibroma (greater than or equal to 2 needed) are 2 of the major criteria for TS. Multiple facial angiofibromas are also found in multiple endocrine neoplasia type 1 (MEN-1) and Birt-Hogg-Dube syndrome. Pearly penile papules are chronic, asymptomatic, papules found on the coronal margin and sulcus of the penis. They are more common in uncircumcised men.
Cutaneous angiofibromas can be located on different areas of the body including the face where they are commonly called fibrous papules or adenoma sebaceum on the penis where they are called pearly penile papules, underneath the nail where they are called periungual angiofibromas or Koenen tumors, and in the mouth where they are called oral fibromas. Facial angiofibromas are considered one of the most obvious clinical presentations of tuberous sclerosis (TS), an autosomal dominant hamartomatous disorder that affects the skin, kidneys, heart, brain, and lungs. With TS, angiofibromas typically arise on the face in childhood and early adulthood. Both facial angiofibromas (greater than or equal to 3 needed) and periungual angiofibroma (greater than or equal to 2 needed) are 2 of the major criteria for TS. Multiple facial angiofibromas are also found in multiple endocrine neoplasia type 1 (MEN-1) and Birt-Hogg-Dube syndrome. Pearly penile papules are chronic, asymptomatic, papules found on the coronal margin and sulcus of the penis. They are more common in uncircumcised men.
1) kanohi – Fibrous papule
2) ure – Pearly penile papule
3) i raro i te matikuku, maikuku matikara rānei – Periungual angiofibroma