Juvenile xanthogranuloma - Xanthogranuloma Taiohi
☆ I te 2022 Stiftung Warentest hua mai i Tiamana, he iti noa iho te pai o nga kaihoko ki a ModelDerm i nga korero mo te waea rongoa utu.
References
Ko te Juvenile xanthogranuloma (JXG) he ahua tino noa me te momo auau non-Langerhans cell histiocytic disorder i roto i nga tamariki. I roto i te 75% o nga keehi, ka kitea enei whiu i roto i te tau tuatahi o te oranga, a, neke atu i te 15-20% o nga turoro ka pa mai i te whanautanga. Ahakoa he onge i roto i nga pakeke, ko te nuinga o nga wa ka puta te JXG ki nga taangata i te mutunga o te rua tekau ki te toru tekau, a ko te nuinga o nga turoro pakeke he kotahi noa te mate. I runga i te haumanu, ka puta he puku kotahi, he maha, he kowhai-karaka-parauri ranei, he putunga maro ranei, i runga i te mata, te kaki, me te tinana o runga. He iti noa nga whiu o te waha engari ka puta he putunga kowhai i nga taha o te arero, i etahi atu waahi ranei o te waha, tera pea ka puta he mate whewhe me te toto. Ko te nuinga o nga wa karekau nga mate kiri e puta mai he tohu, ka ngaro noa atu i roto i nga tau maha. Ahakoa te onge, ko te whai waahi o te mata te take nui atu i tua atu o te kiri, whai muri ko te urunga o te puku. Ko te Ocular JXG ka pa ki te kanohi kotahi anake ka pa ki te iti iho i te 0. 5 % o nga turoro, ahakoa tata ki te 40% o te hunga e pa ana ki te kanohi he maha nga mate kiri ina kitea.
Juvenile xanthogranuloma (JXG) is a relatively common entity and is the most common form of non-Langerhans cell histiocytic disorder of childhood., It is estimated that in 75% of cases, lesions appear during the first year of life, with >15-20% of patients having lesions at birth. JXG is rare in adults, with a peak incidence in the late twenties to thirties. The majority of adult patients have solitary lesions. Typically, the clinical presentation consists of solitary or multiple yellow-orange-brown firm papules or nodules. The most common locations are the face, neck, and upper torso. Oral lesions are rare and often occur as a yellow nodule on the lateral aspects of the tongue. Oral lesions can also arise on the gingival, buccal mucosa, and midline hard palate and may ulcerate and bleed. Cutaneous lesions are usually asymptomatic, and most lesions spontaneously involute over the course of several years. Although occurring rarely, ocular involvement is the most common extracutaneous site involved, followed by the lungs. Ocular JXG is nearly always unilateral and develops in less than 0.5% of patients. Approximately 40% of patients with ocular JXG, however, have multiple cutaneous lesions at the time of diagnosis.
Juvenile xanthogranuloma (JXG) is a relatively common entity and is the most common form of non-Langerhans cell histiocytic disorder of childhood., It is estimated that in 75% of cases, lesions appear during the first year of life, with >15-20% of patients having lesions at birth. JXG is rare in adults, with a peak incidence in the late twenties to thirties. The majority of adult patients have solitary lesions. Typically, the clinical presentation consists of solitary or multiple yellow-orange-brown firm papules or nodules. The most common locations are the face, neck, and upper torso. Oral lesions are rare and often occur as a yellow nodule on the lateral aspects of the tongue. Oral lesions can also arise on the gingival, buccal mucosa, and midline hard palate and may ulcerate and bleed. Cutaneous lesions are usually asymptomatic, and most lesions spontaneously involute over the course of several years. Although occurring rarely, ocular involvement is the most common extracutaneous site involved, followed by the lungs. Ocular JXG is nearly always unilateral and develops in less than 0.5% of patients. Approximately 40% of patients with ocular JXG, however, have multiple cutaneous lesions at the time of diagnosis.
Ko te Juvenile xanthogranulomas (JXGs) he mate noa, he mate ngawari he waahanga o te waahanga nui ake o non-Langerhans cell histiocytoses. I te nuinga o te wa ka kitea he putunga whero, kowhai ranei, ka kitea i runga i te mahunga, i te kaki ranei. Ko te nuinga o nga JXG ka whanake i te whanautanga, i roto ranei i te tau tuatahi o te oranga. Ahakoa he mea rereke, i etahi wa ka pa ki nga waahi o tua atu o te kiri, me te whai waahi o te kanohi hei mea hei mataki e ai ki nga tuhinga o naianei. Ko te tikanga, ko nga JXG i runga i te kiri ka haere noa iho, karekau e hiahia maimoatanga.
Juvenile xanthogranulomas (JXGs) are uncommon, benign diseases that are part of a larger category of non-Langerhans cell histiocytoses. They typically show up as one or more red or yellowish lumps, often found on the head or neck. Most JXGs develop either at birth or within the first year of life. While it's unusual, sometimes they can affect areas beyond the skin, with eye involvement being something to watch for according to existing literature. Generally, JXGs on the skin go away on their own and typically don't need treatment.
Juvenile xanthogranulomas (JXGs) are uncommon, benign diseases that are part of a larger category of non-Langerhans cell histiocytoses. They typically show up as one or more red or yellowish lumps, often found on the head or neck. Most JXGs develop either at birth or within the first year of life. While it's unusual, sometimes they can affect areas beyond the skin, with eye involvement being something to watch for according to existing literature. Generally, JXGs on the skin go away on their own and typically don't need treatment.
Ka kitea te whiu mata ki runga ki te 10% o nga tangata whai JXG ka pa ki o raatau tirohanga. Ahakoa te nuinga o nga wa ka ngaro noa nga whiu kiri, he iti noa te pai ake o nga patunga o te mata me te hiahia maimoatanga.