Lymphangioma
Ko te Lymphangioma he heenga o te punaha lymphatic e tohuhia ana e nga whiu he kiri angiangi te pakitara. Ka puta enei kino i nga tau katoa, ka uru pea ki tetahi wahanga o te tinana, engari 90% ka puta ki nga tamariki kei raro iho i te 2 tau te pakeke, ka uru ki te mahunga me te kaki. Ko nga lymphangiomas ka kitea i mua i te whanautanga ma te whakamahi i te ultrasound fetal. Ko nga lymphangiomas kua riro mai ka puta mai i te whara, i te mumura, i te aukati lymphatic ranei. I te mea karekau he tupono ki te mate kino, ka tukuna nga lymphangiomas mo nga take whakapaipai anake.
☆ I te 2022 Stiftung Warentest hua mai i Tiamana, he iti noa iho te pai o nga kaihoko ki a ModelDerm i nga korero mo te waea rongoa utu.
References
Ko te Lymphangioma e mohiotia ana ano ko te lymphatic malformation (LM) . He mate toto mai i te whanautanga. Ko te ahua o te tipu kino o te kiko lymphatic i mua me muri i te whanautanga. Lymphangioma ka pa ki te 1 i roto i te 2000 ki te 4000 tangata, kaore he rereketanga nui i waenga i nga ira tangata me nga iwi. Ko te nuinga o nga keehi (80–90%) ka tohua i mua i te rua o nga tau. He rereke nga tohu, mai i te pupuhi o te rohe ki te nui o nga rerekee kei roto i nga awa lymphatic, i etahi wa ka puta te pupuhi nui e kiia nei ko te elephantiasis. Hei tauira, lymphangioma i roto i te kaki me te kanohi ka pupuhi te kanohi, a, i nga keehi kino, he ahua kino. Ka pa ana ki te arero, ka tupu te tipu o te kauae me nga niho hee. I roto i te waha me te kaki, ka raru pea te manawa me nga mate ohorere. I roto i nga kanohi, tera pea ka ngaro te tirohanga, te iti o te nekehanga o te kanohi, te heke o nga kamo, me nga kanohi pupuhi. Ko te whai waahi o nga peka ka puta te pupuhi me te tipu rerekee o nga kopa me nga wheua. Ko te nuinga o te wa ka puhoi te tipu o tenei puku, engari ko nga mate, ko nga huringa homoni, ko te whara ranei ka tere te tipu, ka puta he mate whakamomori me mate wawe.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
I roto i tenei rangahau whakamuri, i arotakehia e matou e 24 nga tamariki kua lymphangioma me te rongoa ki te werohanga wairewa bleomycin mai i Hanuere 1999 ki Hakihea 2004. Ko te nuinga o nga whiu (63%) kua ngaro katoa, 21% i pai te whakautu, 16% kaore i pai te whakautu. Tokorua nga turoro i hoki mai te puku i muri mai, ka rua etahi atu i mate puku i reira i werohia ai. Waimarie, karekau matou i kite i etahi atu raru nui me nga paanga taha.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
Ko nga momo matua o lymphangioma e whai ake nei - lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Ko enei kei te 26% o nga pukupuku pukupuku ngawari i roto i nga tamariki engari he iti noa iho i nga pakeke. Ko te lymphangioma circumscriptum , ko te momo tino auau, e whakaatu ana i nga ngongo lymphatic e puta mai ana i roto i te kiri, e hanga ana i nga wiwi ki tonu i te wai e rite ana ki te tipu o te poroka, me te pupuhi kiko. I te nuinga o te wa ka kitea i runga i nga waahi he nui te kupenga lymphatic penei i nga peka, katua, me nga papa. I haere mai tetahi wahine 71-tau te pakeke ki ta matou whare haumanu me te pupuhi tonu o nga waewae, nga puku mawhero i runga i ona ira, te patito, me te rere o te wai rewharewha. I tangohia e matou nga puku katoa me te tikanga e kiia nei ko bilateral major labiectomy, ka tu ki te taumata fascia o Colles, me te pupuri i te clitoris me te fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
