Lymphangioma - Limfanġjoma
Limfanġjoma (Lymphangioma) huma malformazzjonijiet tas-sistema limfatika kkaratterizzati minn leżjonijiet li huma ċisti b'ħitan irqaq. Dawn il-malformazzjonijiet jistgħu jseħħu fi kwalunkwe età u jistgħu jinvolvu kwalunkwe parti tal-ġisem, iżda 90% jseħħu fi tfal ta 'inqas minn sentejn u jinvolvu r-ras u l-għonq. Limfangiomi huma komunement dijanjostikati qabel it-twelid bl-użu ta' ultrasonografija tal-fetu. Limfangiomi miksuba jistgħu jirriżultaw minn trawma, infjammazzjoni, jew ostruzzjoni limfatika. Peress li m'għandhom l-ebda ċans li jsiru malinni, il-limfangiomi normalment jiġu ttrattati għal raġunijiet kożmetiċi biss.
☆ Fir-riżultati ta' Stiftung Warentest tal-2022 mill-Ġermanja, is-sodisfazzjon tal-konsumatur b'ModelDerm kien biss ftit inqas milli b'konsultazzjonijiet bit-telemediċina mħallsa.
References
Lymphangioma hija magħrufa wkoll bħala malformazzjoni limfatika (LM) . Huwa disturb vaskulari preżenti mit-twelid. Huwa kkaratterizzat minn tkabbir anormali tat-tessut limfatiku qabel u wara t-twelid. Lymphangioma taffettwa madwar 1 minn 2000 sa 4000 ruħ, mingħajr ebda differenza sinifikanti bejn is-sessi jew ir-razzez. Ħafna mill-każijiet (80-90%) jiġu djanjostikati qabel it-tnejn. Is-sintomi jvarjaw ħafna, minn nefħa lokalizzata għal anormalitajiet estensivi fil-kanali limfatiċi, li xi drabi jwasslu għal nefħa severa magħrufa bħala elephantiasis. Pereżempju, lymphangioma fl-għonq u fil-wiċċ jista 'jikkawża nefħa tal-wiċċ, u f'każijiet severi, sfigurazzjoni. Meta taffettwa l-ilsien, jista 'jwassal għal tkabbir żejjed tax-xedaq u snien allinjati ħażin. Fil-ħalq u l-għonq, jista 'jikkawża problemi tan-nifs u emerġenzi ta' theddida għall-ħajja. Fl-għajnejn, jista 'jikkawża telf tal-vista, moviment limitat tal-għajnejn, tebqet il-għajn imdendla, u għajnejn minfuħa. L-involviment tar-riġlejn jista' jikkawża nefħa u tkabbir anormali tat-tessuti u l-għadam. Dan it-tumur ġeneralment jikber bil-mod, iżda infezzjonijiet, bidliet ormonali, jew korriment jistgħu jikkawżaw tkabbir rapidu, li joħolqu riskji ta 'theddida għall-ħajja li jeħtieġu trattament urġenti.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
F'dan l-istudju retrospettiv, aħna rrevejna 24 tifel li kellhom lymphangioma u ġew ikkurati b'injezzjonijiet ta 'soluzzjoni ta' bleomycin minn Jannar 1999 sa Diċembru 2004. Ħafna mill-leżjonijiet (63%) marru kompletament, 21% kisbu rispons tajjeb, u 16% ma weġibx tajjeb. Żewġ pazjenti kellhom it-tumur lura aktar tard, u tnejn oħra kisbu axxessi fejn ħadu l-injezzjonijiet. Fortunatament, ma rajna l-ebda problemi kbar jew effetti sekondarji oħra.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
It-tipi ewlenin ta ' lymphangioma huma kif ġej - lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Dawn jiffurmaw madwar 26% tat-tumuri vaskulari beninni fit-tfal iżda huma inqas komuni fl-adulti. Lymphangioma circumscriptum , it-tip l-aktar frekwenti, juri kanali limfatiċi jisporġu 'l barra mill-ġilda, li jiffurmaw vesikuli ċari mimlija fluwidu simili għal spawn taż-żrinġ, flimkien ma' nefħa tat-tessut. Tipikament jidher fuq żoni b'netwerk limfatiku għani bħar-riġlejn, it-tronk, u l-armpits. Mara ta’ 71 sena ġiet il-klinika tagħna b’nefħa persistenti fir-riġlejn, ħotob roża fuq il-ġenitali tagħha, ħakk, u jnixxi fluwidu limfatiku. Aħna neħħejna kirurġikament il-ħotob kollha bi proċedura msejħa labiectomy maġġuri bilaterali, nieqfu fil-livell tal-fascia ta 'Colles, filwaqt li ppreservajna l-klitoris u fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
