Neurofibromatosishttps://en.wikipedia.org/wiki/Neurofibromatosis_type_I
Neurofibromatosis ndi vuto la mitundu yambiri la munthu lomwe limachitika chifukwa cha kusintha kwa neurofibromin. Neurofibromatosis imayambitsa zotuta m'mitsempha yamanja zomwe zimatha kukula kulikonse m'thupi. Ndi imodzi mwa zovuta zofala kwambiri za majini komanso vuto lalikulu la autosomal.

Zizindikiro zodziwika bwino za Neurofibromatosis zimaphatikizira ma Lisch nodules, neurofibromas, ma café au lait spots, Scoliosis (kupindika kwa msana), kulephera kuphunzira, kusokonekwa kwa masomphenya, kulumala kwamaganizidwe, ndi khunyu.

Palibe chithandizo chenichenicho mpaka pano.

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  • Cafe au lait macules zowoneka mu Neurofibromatosis type 1 (NF-1)
  • Ma neurofibroma ambiri (Von Recklinghausen disease)
  • Neurofibroma
  • Ma neurofibromas angapo ali ang'onoang'ono.
  • NF-1: Wodwala okalamba kumbuyo.
  • Chiwonetsero cha NF-1 chimachitika bwino. Neurofibromas angapo amawonedwa ndi utoto wamawanga.
  • Angiofibroma ya nkhope imachitika chifukwa cha tuberous sclerosis.
References Neurofibromatosis 29083784 
NIH
Neurofibromatosis ndi vuto lomwe limayambitsa zotupa mu dongosolo la m'manja ndi khungu. Mtundu 1 umakhala wotengera kwambiri ndipo umasonyeza zizindikiro monga neurofibromas, café‑au‑lait spots, freckling, ndi optic gliomas. Zizindikirozi zimakhala zachipatala. Mtundu 2, kumbali ina, imalembedwa ndi bilateral vestibular schwannomas (VS) ndi meningiomas, zomwe zimawonjezera chiopsezo cha cholowa kwambiri. Kuyang'anira kumaphatikizapo kuyang'anira nthawi zonse ndi chithandizo cha mankhwala monga kufunika kwa mitundu yonse ya neurofibromatosis.
Neurofibromatosis is a neurocutaneous disorder characterized by tumors in the nervous system and skin. Neurofibromatosis types 1 and 2 are the most common and are distinct entities. Neurofibromatosis type 1, or von Recklinghausen disease, is an autosomal dominant disease. Neurofibromatosis type 1 presents with neurofibromas, cafe-au-lait macules, freckling, and optic gliomas. It is a clinical diagnosis. Neurofibromatosis type 2 (NF2) is a disease characterized by bilateral vestibular schwannomas (VS) and meningiomas. It has an autosomal dominant inheritance pattern. Treatment for neurofibromatosis types 1 and 2 is clinical monitoring and medical intervention when appropriate.