Lymphangioma
Lymphangioma o fa'aletonu o le faiga o le lymphatic e fa'aalia i manu'a e manifinifi puipui. O nei faaletonu e mafai ona tupu i soo se matua ma e ono aʻafia ai soʻo se vaega o le tino, ae o le 90% e tupu i tamaiti e itiiti ifo i le 2 tausaga le matutua ma aofia ai le ulu ma le ua. O le lymphangiomas e masani ona maua aʻo leʻi fanau mai e faʻaaoga ai le ultrasonography fetal. O lymphangiomas e maua e ono mafua mai i manu'a, fula, po'o le fa'alavelave ole lymphatic. Talu ai e leai se avanoa e fa'ama'i ai, o le lymphangiomas e masani lava ona togafitia mo na'o mafua'aga fa'alelei.
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References
Lymphangioma o lo'o ta'ua fo'i o le lymphatic malformation (LM) . O se fa'alavelave fa'alavalava o lo'o iai mai le fanau mai. O lo'o fa'aalia i le tupu fa'afuase'i ole aano o le lymphatic a'o le'i fanau mai ma pe a uma. Lymphangioma a'afia pe tusa ma le 1 i le 2000 i le 4000 tagata, e leai se eseesega tele i le va o itupa po'o ituaiga. O le tele o mataupu (80-90%) e maua a'o le'i lua tausaga. O auga e eseese tele, mai le fula fa'apitonu'u i le tele o fa'alavelave i le ala o le lymphatic, o nisi taimi e o'o atu ai i le fula matuia e ta'ua o le elefantiasis. Mo se faʻataʻitaʻiga, lymphangioma i le ua ma foliga e mafai ona tupu ai le fulafula o foliga, ma i tulaga ogaoga, faʻaleagaina. A afaina ai le laulaufaiva, e mafai ona tupu tele ai le auvae ma le sa'o o nifo. I le gutu ma le ua, e mafai ona mafua ai faafitauli o le manava ma faʻalavelave faʻafuaseʻi e lamatia ai le ola. I mata, e mafai ona mafua ai le leiloa o le vaʻai, faʻatapulaʻa le gaioiga o mata, laumata faʻafefe, ma mata faʻafefe. O le a'afia o vae e mafai ona tupu ai le fula ma le tupu fa'aletonu o a'ano ma ponaivi. O lenei tuma e masani ona tupu lemu, ae o faʻamaʻi pipisi, suiga o le hormonal, poʻo manuʻa e mafai ona mafua ai le tuputupu aʻe vave, ma faʻaalia ai lamatiaga e lamatia ai le ola e manaʻomia ai togafitiga faʻanatinati.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
I lenei suʻesuʻega lata mai, na matou iloiloina ai tamaiti e 24 na maua lymphangioma ma togafitia i tui o le bleomycin solution mai Ianuari 1999 ia Tesema 2004. O le tele o faʻamaʻi (63%) na alu ese atoa, 21% na maua se tali lelei, ma 16% e le'i tali lelei mai. E to'alua tagata mama'i na toe fo'i mai le tuma mulimuli ane, ae to'alua na maua i le manava lea na latou tui ai. O le mea e laki ai, matou te leʻi vaʻaia ni isi faʻafitauli tetele poʻo ni aʻafiaga.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
O ituaiga autu o lymphangioma e fa'apea - lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. O nei mea e aofia ai le 26% o tuma vascular benign i tamaiti ae e le masani ai i tagata matutua. Lymphangioma circumscriptum , o le ituaiga masani, e faʻaalia ai ala lymphatic o loʻo faʻapupulaina i totonu o le paʻu, faʻatupu ai ni vesikeli manino e tumu i le vai e tutusa ma le fula o le tino. E masani lava ona aliali mai i vaega o loʻo iai le tele o fesoʻotaʻiga lymphatic e pei o vae, ogalaau, ma lima. Na sau se fafine e 71 tausaga le matua i le matou falemaʻi ma le fula pea o vae, patupatu piniki i ona itutinosa, mageso, ma le sua o le lymph. Na matou aveese uma patupatu i se taotoga e ta'ua o le bilateral major labiectomy, ma taofi i le tulaga o Colles' fascia, a'o fa'asaoina le clitoris ma le fachette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
