Neurofibroma o le ma'i tumo neura fa'a'ofu'ofu i totonu o le tino. I le 90% o mataupu, o tuma tutoʻatasi e aunoa ma ni faʻafitauli faʻapitoa. Ae ui i lea, o le vaega o totoe e maua i tagata o le neurofibromatosis type I (NF1), o se ma'i autosomal. E mafai ona maua le tele o fa'ailoga ona o le fa'aleagaina o le tino ma le tiga i le le atoatoa o le mafaufau.
Neurofibroma e mafai ona lautele i le 2 i le 20 mm, e malu, pa'epa'e, ma piniki‑pa'epa'e. E mafai ona fa'aoga se biopsy mo su'esu'ega o le histopathology.
Neurofibroma e masani ona tupu i tausaga o le talavou ma e masani ona tupu pe a uma le talavou. I tagata o lo'o i le Neurofibromatosis Type I, latou te faaauau pea ona faateleina le numera ma le lapopoa i le taimi o le matua.
A neurofibroma is a benign nerve-sheath tumor in the peripheral nervous system. In 90% of cases, they are found as stand-alone tumors, while the remainder are found in persons with neurofibromatosis type I (NF1), an autosomal-dominant genetically inherited disease. They can result in a range of symptoms from physical disfiguration and pain to cognitive disability.
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O le neurofibroma o le tagata maʻi e maua i le neurofibromatosis.
Neurofibromas e masani ona leaga pe a matua. O manu'a i lenei tagata na muamua aliali mai, ma le talavou o ia.
Solitary neurofibroma — O se papule erythematous (vaivai).
Neurofibromas o tuma masani e maua i neura peripheral. E masani lava e pei o patupatu vaivai i luga o le pa'u po'o, ma e mafai ona tupu i tama'i i lalo. E atia'e mai le endoneurium, ma o le ituaiga feso'ota'i o le si'omia ai fa'afu o neura peripheral. Neurofibromas are the most prevalent benign peripheral nerve sheath tumor. Often appearing as a soft, skin-colored papule or small subcutaneous nodule, they arise from endoneurium and the connective tissues of peripheral nerve sheaths.
Neurofibroma e mafai ona lautele i le 2 i le 20 mm, e malu, pa'epa'e, ma piniki‑pa'epa'e. E mafai ona fa'aoga se biopsy mo su'esu'ega o le histopathology.
Neurofibroma e masani ona tupu i tausaga o le talavou ma e masani ona tupu pe a uma le talavou. I tagata o lo'o i le Neurofibromatosis Type I, latou te faaauau pea ona faateleina le numera ma le lapopoa i le taimi o le matua.