Neurofibromatosishttps://en.wikipedia.org/wiki/Neurofibromatosis_type_I
Neurofibromatosis yakaoma multi‑system disorder yevanhu inokonzerwa nekuchinja kwe neurofibromin. Neurofibromatosis inokonzeresa mapundu pamwe netsinga dzinogona kukura chero pamuviri. Neurofibromatosis ndeimwe yeanowanzozivikanwa genetic kusagadzikana uye autosomal dominant disorder.

Zviratidzo zvinowanzoonekwa zve neurofibromatosis zvinosanganisira mavara matsvuku‑tsvuku muchikamu cheziso, anodaidzwa kuti Lisch nodules, pamwe ne neurofibromas. Scoliosis (kukombama kwemusana), kurema pakudzidza, kusaona zvakanaka, kurema mupfungwa, nzvimbo dzakawanda dzekofi kana pfari zvinogona kuperekedzwawo.

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  • Cafe au lait macule inowanikwa muNeurofibromatosis type 1 (NF-1)
  • Multiple Neurofibromas (Neurofibroma dzakawanda) (Von Recklinghausen disease)
  • Neurofibroma
  • Neurofibroma dzakawanda diki.
  • NF-1 ― Murwere ane musana wakakura.
  • Kuratidzwa kweNF-1 kwakajairika. Nhamba ye neurofibromas inocherechedzwa iine mavara.
  • Murwere ane angiofibroma pachiso, zvinokonzerwa ne tuberous sclerosis.
References Neurofibromatosis 29083784 
NIH
Neurofibromatosis is a condition inokonzeresa mapundu pamitsara yeganda. Type 1 inogara nhaka zvakanyanya uye inoratidza zviratidzo zvakaita se neurofibromas, café‑au‑lait spots, freckling, uye optic gliomas. Kuongororwa kunobva pane zviratidzo zvekliniki. Type 2, kune rumwe rutivi, inobatanidzwa ne bilateral vestibular schwannomas (VS) uye meningiomas, uye zvakare inogara nhaka zvakanyanya. Kutungamira kunosanganisira kuongorora nguva dzose uye kurapwa sezvinodiwa kune ese marudzi e neurofibromatosis.
Neurofibromatosis is a neurocutaneous disorder characterized by tumors in the nervous system and skin. Neurofibromatosis types 1 and 2 are the most common and are distinct entities. Neurofibromatosis type 1, or von Recklinghausen disease, is an autosomal dominant disease. Neurofibromatosis type 1 presents with neurofibromas, cafe-au-lait macules, freckling, and optic gliomas. It is a clinical diagnosis. Neurofibromatosis type 2 (NF2) is a disease characterized by bilateral vestibular schwannomas (VS) and meningiomas. It has an autosomal dominant inheritance pattern. Treatment for neurofibromatosis types 1 and 2 is clinical monitoring and medical intervention when appropriate.