Amyloidosishttps://en.wikipedia.org/wiki/Amyloidosis
Amyloidosis waa koox cuduro ah oo ay ku urursan yihiin borotiinno aan caadi ahayn, oo loo yaqaan amyloid fibrils, kuwaas oo ku dhisma unugyada. Papules hyperkeratitis leh oo cuncun leh, kuwaas oo laga yaabo inay isku duubmaan oo sameeyaan balamo cawl iyo bunni ah. Goobaha caadiga ah ee uu cudurku ku dhaco waa tibiae hore iyo dhabarka sare.

Ogaanshaha iyo daawaynta
#Electrophoresis of blood or urine
#Skin biopsy
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  • Astaamaha caadiga ah ee wajiga ee Amyloidosis
  • Aragtida la weyneeyey, papules adag oo qaab la mid ah ayaa lagu arkay. Waxay yihiin kuwo lebbis ah oo adag, si ka duwan xanuunada xasaasiyadda sida maqaarka (atopic dermatitis).
  • Astaamaha maqaarka ee amyloidosis cutis dyschromica — (A) Macules midab leh oo ku yaal lugta hoose.
  • Lichen amyloidosis inta badan waxaa si khaldan loo ogaadaa iyadoo loo malaynayo inuu yahay maqaarka (atopic dermatitis). Kiis caadi ah wuxuu keenaa papules yar yar oo adag iyo cuncun.
  • Nabarka Amyloidosis wuxuu u ekaan karaa maqaarka maqaarka (atopic dermatitis).
References Lichen amyloidosis - Case reports 24130236 
NIH
Naag 26 jir ah ayaa noo timid rugta caafimaadka iyadoo ka cabanaysa finan cuncun oo lugaha ka soo baxay, kuwaas oo ay lahayd muddo 10 sano ah. In kasta oo la isticmaalay kiriimyada steroid-ka iyo kareemka tazarotene, finanku ma rayn. Ma aysan lahayn taariikh qoys oo khuseeya. Markii aanu baadhnay, waxa aanu ka helnay balamo sare oo lugaha hore kaga yaal, kuwaas oo u dhigma cudurka lichen amyloidosis.
A 26-year-old woman presented to our clinic with an itchy rash on her legs that had persisted for 10 years. The rash had previously been treated with topical steroids and tazarotene cream, with no improvement. The patient’s family history was noncontributory. A physical examination showed discrete and coalescing hyperkeratotic tan-brown papules on the pretibial surfaces, consistent with lichen amyloidosis.
 Lichen Amyloidosis: Towards Pathogenesis-Driven Targeted Treatment 36763750 
NIH
Lichen Amyloidosis waa xaalad maqaarka ah oo naadir ah, waxaana lala xiriiriyaa cuncun joogto ah oo aan la garanayn sababta. Caadi ahaan, waxay u soo baxdaa sidii kooxo kor u kaca, balastar midab leh oo ku yaal maqaarka kore. Lichen Amyloidosis inta badan waxay ku dhacdaa dadka da'doodu u dhaxayso 50 ilaa 60 sano. Nasiib darro, weli wax daawo ah lagama heli karo; daawaynta hadda la heli karo badankood si fiican uma shaqeeyaan.
Lichen Amyloidosis (LA) is an uncommon, primary cutaneous amyloidosis associated with chronic, idiopathic pruritus. Clinical presentation of LA includes skin colored to hyperpigmented, papules coalescing into plaques with a rippled appearance on the extensors.1 LA most commonly presents in the fifth to sixth decade of life and has no curative treatments. Overall response to current therapies is poor.
 Clinical Characteristics of Lichen Amyloidosis Associated with Atopic Dermatitis: A Single Center, Retrospective Study 38086357 
NIH
Lichen amyloidosis waa xaalad maqaarka cuncun oo raagta. Waxay caan ku tahay rucubyada kuuskuus dhumuc weyn leh oo inta badan laga helo dhabarka, shilalka, bowdada, iyo gacmaha. Marka lagu baaro mikroskoob, Lichen amyloidosis waxay muujinaysaa ururinta amyloid ee lakabka sare ee maqaarka oo ay weheliso dhumuc iyo ballaadhinta lakabka sare ee maqaarka. In kasta oo sababta saxda ah ee Lichen amyloidosis aan weli si buuxda loo fahmin, cilmi‑baadhisyo hore ayaa ku xidhay arrimo ay ka mid yihiin xoqidda maqaarka, dhimashada unugyada, caabuqyada fayraska, iyo kuwa kale. Lichen amyloidosis waxay u muuqataa inay ku xidhan tahay dhowr xaaladood oo maqaarka ah (atopic dermatitis, lichen planus, mycosis fungoides).
Lichen amyloidosis (LA) is a chronic pruritic skin disorder characterized by multiple grouped hyperkeratotic papules, predominantly located on the back, shins, thighs, and arms. Histological analysis of LA shows amyloid deposition in the papillary dermis and hyperkeratosis and acanthosis of the epidermis. The exact pathogenesis of LA has not yet been elucidated; however, prior reports have implicated frictional epidermal damage, apoptosis, viral infection, and many other triggers. LA is reportedly associated with several skin disorders, including atopic dermatitis (AD), lichen planus, and mycosis fungoides.