Juvenile xanthogranuloma - Xanthogranuloma Dhallinta
https://en.wikipedia.org/wiki/Juvenile_xanthogranuloma
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Nodulka jaallaha ee carruurta, caadi ahaan Xanthogranuloma Dhallinta (Juvenile xanthogranuloma).
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References
Juvenile Xanthogranuloma 30252359 NIH
Juvenile xanthogranuloma (JXG) waa xaalad caadi ah oo ah nooca ugu badan ee non-Langerhans cell histiocytic disorder ee carruurta. Qiyaastii 75% kiiska, nabarradani waxay soo baxaan sannadka ugu horreeya ee nolosha, halka in ka badan 15–20% bukaanada ay ka bilaabmaan dhalashada. In kasta oo ay naadir ku tahay dadka waaweyn, JXG waxay caadi ahaan ku dhacdaa dadka da'doodu u dhaxayso labaatan ilaa soddon sano, waxaana inta badan bukaanada qaangaarka ah ay leeyihiin hal dhaawac. Markaa laga eego dhinaca klinikada, waxay u muuqataa hal ama dhowr burooyin jaalle‑orange‑brown ah, inta badan ku yaal wejiga, qoorta, iyo qaybta kore ee jirka. Burooyinka afka waa kuwo aan caadi ahayn, balse waxay u muuqan karaan sida burooyin jaalle ah oo ku yaal dhinacyada carrabka ama meel kale oo afka ah, waxaana ay keeni karaan boogo iyo dhiig‑bax. Burooyinka maqaarka badanaa ma keeni karaan calaamado, waxayna u muuqdaan inay si iskeed ah u baaba'aan dhowr sano gudahood. In kasta oo ay naadir tahay, ka qaybgalka indhaha waa arrinta ugu badan ee ka baxsan maqaarka, waxaana ku xiga ka qaybgalka sanbabada. Ocular JXG caadi ahaan waxay saameysaa hal indho oo keliya, waxaana ay ku dhacdaa in ka yar 0.5% bukaanada; si kastaba ha ahaatee, qiyaastii 40% dadka ay indhahoodu ku lug leeyihiin ayaa sidoo kale leh burooyin badan oo maqaarka ah marka la ogaado.
Juvenile xanthogranuloma (JXG) is a relatively common entity and is the most common form of non-Langerhans cell histiocytic disorder of childhood., It is estimated that in 75% of cases, lesions appear during the first year of life, with >15-20% of patients having lesions at birth. JXG is rare in adults, with a peak incidence in the late twenties to thirties. The majority of adult patients have solitary lesions. Typically, the clinical presentation consists of solitary or multiple yellow-orange-brown firm papules or nodules. The most common locations are the face, neck, and upper torso. Oral lesions are rare and often occur as a yellow nodule on the lateral aspects of the tongue. Oral lesions can also arise on the gingival, buccal mucosa, and midline hard palate and may ulcerate and bleed. Cutaneous lesions are usually asymptomatic, and most lesions spontaneously involute over the course of several years. Although occurring rarely, ocular involvement is the most common extracutaneous site involved, followed by the lungs. Ocular JXG is nearly always unilateral and develops in less than 0.5% of patients. Approximately 40% of patients with ocular JXG, however, have multiple cutaneous lesions at the time of diagnosis.
Juvenile Xanthogranuloma: An Entity With a Wide Clinical Spectrum 32721389Juvenile xanthogranulomas (JXGs) waa cudurro aan caadi ahayn oo ka tirsan qaybta weyn ee non-Langerhans cell histiocytoses. Badanaa waxay u muuqdaan hal ama in ka badan oo leh boogo cas ama huruud ah, oo inta badan laga helo madaxa ama qoorta. JXG-yada badankoodu waxay bilaabaan inay soo baxaan marka ay dhashaan ama sannadka ugu horreeya ee nolosha. Inkasta oo ay yihiin wax aan caadi ahayn, mararka qaarkood waxay saameyn karaan meelaha ka baxsan maqaarka, iyada oo ay ku lug leedahay indhaha, taas oo ah wax la daawado sida ku cad suugaanta jirta. Guud ahaan, JXG-yada maqaarka waxay si iskiis ah u baaba'aan oo caadi ahaan uma baahna daaweyn.
Juvenile xanthogranulomas (JXGs) are uncommon, benign diseases that are part of a larger category of non-Langerhans cell histiocytoses. They typically show up as one or more red or yellowish lumps, often found on the head or neck. Most JXGs develop either at birth or within the first year of life. While it's unusual, sometimes they can affect areas beyond the skin, with eye involvement being something to watch for according to existing literature. Generally, JXGs on the skin go away on their own and typically don't need treatment.
Dhaawaca indhaha waxa uu ku dhaca ilaa 10% dadka qaba JXG, wuxuuna waxyeeli karaa aragtidooda. In kasta oo nabarada maqaarku ay caadi ahaan iskood u baaba'aan, nabarada indhaha si kedis ah ayay u roonaadaan waxayna u baahan yihiin daaweyn.