Lymphangioma
https://en.wikipedia.org/wiki/Lymphangioma
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References
Recent Progress in Lymphangioma 34976885 NIH
Lymphangioma waxaa sidoo kale loo yaqaannaa lymphatic malformation (LM). Waa xanuun ku dhaca xididdada dhiigga laga bilaabo dhalashada. Waxaa lagu gartaa koritaanka aan caadiga ahayn ee unugyada lymphatic ka hor iyo ka dib dhalashada. Lymphangioma waxay saamaysaa qiyaastii 1 qof oo ka mid ah 2 000–4 000, iyada oo aan farqi u lahayn lab iyo dheddig ama isir. Kiisaska intooda badan (80‑90 %) waxaa la ogaadaa ka hor inta aysan gaarin da’da laba sano. Calaamadaha way aad u kala duwan yihiin, laga bilaabo bararka gudaha ilaa cillado badan oo ka yimaada kanaalada lymphatic, mararka qaarkoodna waxay keeni karaan barar daran oo loo yaqaan elephantiasis. Tusaale ahaan, lymphangioma qoorta iyo wejiga waxay keeni karaan barar wejiga, iyo xaaladaha daran, cillad. Marka ay saameyn ku yeelato carrabka, waxay u horseedi kartaa daanka oo kor u kaca iyo ilkaha oo aan hagaagsanayn. Afka iyo qoorta, waxay keeni karaan dhibaatooyin neefsashada ah iyo xaalado degdeg ah oo nafta halis gelinaya. Indhaha, waxay keeni karaan lumis arag, dhaqdhaqaaqa indhaha oo xaddidan, daboolka indhaha oo sii dhacaya, iyo indho bararsan. Ku lug lahaanshaha addimada waxay keeni kartaa barar iyo korriin aan caadi ahayn ee unugyada iyo lafaha. Buradani badanaa si tartiib‑tartiib ah ayey u koraan, laakiin caabuqa, isbeddelada hormoonnada, ama dhaawaca ayaa keeni kara korriin degdeg ah, taasoo dhalin karta khataro nafta halis gelinaya oo u baahan daaweyn degdeg ah.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma: Is intralesional bleomycin sclerotherapy effective? 22279495 NIH
Daraasaddan dib-u-eegista ah, waxaan dib u eegnay 24 carruur ah oo qaba lymphangioma, waxaana lagu daweeyay irbado bleomycin laga bilaabo Janaayo 1999 ilaa Diseembar 2004. Inta badan nabarada (63%) gabi ahaanba way baaba'een, 21% waxay heleen jawaab celin wanaagsan, halka 16% aysan si fiican uga jawaabin. Laba bukaan ayaa buro dib ugu soo laabatay waqti dambe, laba kalena waxay ka soo muuqdeen nabarro meesha laga muday. Nasiib wanaag, ma aanan arkin dhibaatooyin kale oo waaweyn ama waxyeelooyin kale.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
Surgical Resection of Acquired Vulvar Lymphangioma Circumscriptum - Case reports 24665431 NIH
Noocyada ugu waaweyn ee lymphangioma waa sida soo socota – lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Kuwani waxay ka kooban yihiin ku dhawaad 26 % burooyinka xididdada dhiigga ee aan fiicnayn ee carruurta, laakiin kuma badna dadka waaweyn. Lymphangioma circumscriptum, nooca ugu badan, ayaa muujinaya dhuumaha limfatic ee ka soo baxa maqaarka, samaynta xuubka dheecaanka ka buuxo oo nadiif ah, oo la mid ah taranka raaga, oo ay weheliso barar nudaha. Waxay caadi ahaan ka soo baxdaa meelaha leh shabakad qani ah sida addimada, jirridda, iyo kilkilooyinka. Haweeney 71 jir ah ayaa noo timid rugta iyadoo lugaha ay barar joogto ah leedahay, kuuskuus casaan ah oo ku yaal xubinta taranka, cuncun, iyo dheecaan limfa ah oo ka soo baxaya. Waxaan si qalliin ah uga saarnay kuuskuusyada oo dhan annagoo adeegsanayna habraac loo yaqaan labiectomy weyn oo laba‑geesood ah, iyadoo la joogsanayo heerka Colles' fascia, lana ilaalinayo kintirka iyo afar‑chetka.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.