Urticaria pigmentosa - Cudurka Urtikaria Pigmentosa
Cudurka Urtikaria Pigmentosa (Urticaria pigmentosa) waa nooca ugu badan ee mastocytosis maqaarka. Waa cudur naadir ah oo ay sababaan tirada xad-dhaafka ah ee unugyada mastarada maqaarka kuwaas oo soo saara cuncun ama nabar maqaarka marka ay xanaaqaan. Baro casaan ama bunni ah ayaa inta badan lagu arkaa maqaarka, sida caadiga ah agagaarka laabta, wejiga, iyo dhabarka. Unugyadan mastarada ah, marka ay cadhoodaan (tusaale, xoqidda maqaarka, kulaylka soo-gaadhista), waxay soo saaraan histamine aad u badan, taasoo kicisa fal-celin xasaasiyadeed taas oo u horseedda finan ku yaal agagaarka aagga xanaaqa, mararka qaarkood loo yaqaan "calaamadaha Darier".
☆ Natiijooyinka Stiftung Warentest ee 2022 ee ka yimid Jarmalka, ku qanacsanaanta macaamilka ee ModelDerm ayaa waxyar uun ka hooseysay la-talinta telemedicine-ka ee lacagta lagu bixiyo.
Waxay u badan tahay inay ku dhacdo jidhka carruurta yaryar.
References
Mastocytosis waa xaalad ay ku badan yihiin unugyada mastarada, oo inta badan laga helo qaybaha kala duwan ee jirka sida maqaarka, dhuuxa lafta, iyo habka dheefshiidka. Sida laga soo xigtay Ururka Caafimaadka Adduunka (WHO) , cutaneous mastocytosis waxaa loo kala saari karaa saddex nooc oo waaweyn. Nooca koowaad (mastocytomas) wuxuu ka kooban yahay keligiis ama dhowr (≤3) nabarro ah. Nooca labaad (urticaria pigmentosa) wuxuu ku lug leeyahay nabaro badan, oo caadi ahaan u dhexeeya in ka badan 10 ilaa in ka yar 100. Nooca ugu dambeeya wuxuu muujinayaa ka qaybqaadashada baahsan ee maqaarka oo dhan. Urticaria pigmentosa waa nooca ugu badan ee mastocytosis maqaarka ee carruurta, laakiin sidoo kale waxay ku dhici kartaa dadka waaweyn. Caadiyan waa xaalad aan dhib lahayn oo inta badan soo roona inta lagu jiro qaan-gaarnimada. Si ka duwan mastocytosis dadka waaweyn, urticaria pigmentosa dhif ayuu u saameeyaa xubnaha gudaha. Mid ka mid ah sifooyin gaar ah oo urticaria pigmentosa ah ayaa ah u janjeera inuu keeno dhibco yar yar, cuncun, bunni guduudan, ama dhibco jaale-brown ah ama nabarro maqaarka ah, oo loo yaqaan finan maqaarka ah. Dhibcahani waxay inta badan soo baxaan caruurnimada waxayna socon karaan nolosha oo dhan.
Mastocytosis is a disorder characterized by mast cell accumulation, commonly in the skin, bone marrow, gastrointestinal (GI) tract, liver, spleen, and lymphatic tissues. The World Health Organization (WHO) divides cutaneous mastocytosis into 3 main presentations. The first has solitary or few (≤3) lesions called mastocytomas. The second, urticaria pigmentosa (UP), involves multiple lesions ranging from >10 to <100 lesions. The last presentation involves diffuse cutaneous involvement. UP is the most common cutaneous mastocytosis in children, but it can form in adults as well. It is considered a benign, self-resolving condition that often remits in adolescence. Unlike adult forms of mastocytosis, there is rarely any internal organ involvement in UP. What makes UP particularly distinctive is its tendency to manifest as small, itchy, reddish-brown, or yellowish-brown spots or lesions on the skin, commonly referred to as urticaria or hives. These spots typically appear in childhood and can persist throughout a person's life.
Mastocytosis is a disorder characterized by mast cell accumulation, commonly in the skin, bone marrow, gastrointestinal (GI) tract, liver, spleen, and lymphatic tissues. The World Health Organization (WHO) divides cutaneous mastocytosis into 3 main presentations. The first has solitary or few (≤3) lesions called mastocytomas. The second, urticaria pigmentosa (UP), involves multiple lesions ranging from >10 to <100 lesions. The last presentation involves diffuse cutaneous involvement. UP is the most common cutaneous mastocytosis in children, but it can form in adults as well. It is considered a benign, self-resolving condition that often remits in adolescence. Unlike adult forms of mastocytosis, there is rarely any internal organ involvement in UP. What makes UP particularly distinctive is its tendency to manifest as small, itchy, reddish-brown, or yellowish-brown spots or lesions on the skin, commonly referred to as urticaria or hives. These spots typically appear in childhood and can persist throughout a person's life.
Gabar 6 jir ah ayaa la soo gashay dhowr bar oo midab madow ah oo markii hore ka soo baxay madaxeeda ka dibna ku faafay wejiga iyo jirkeeda lixdii bilood ee la soo dhaafay. Waxay sheegtay in ay dareemayso in ay kor u kacayaan, isu rogeen casaan, iyo cuncun markii cadaadis la saaray. Ma aysan la kulmin biyo raacid, matag, shuban, ama hiinraag, iyo taariikhdeeda caafimaad ee shaqsiyadeed iyo qoyskeeda ma aysan bixin tilmaamo khuseeya. Markii la baaray, waxaan helnay dhibco madow oo badan oo ku yaal madaxa, foodda, wejiga, iyo qoorta, oo ay la socdaan balamo madow oo xoogaa kor u kacay oo laabta iyo dhabarka ah. Dhibcaha oo si khafiif ah loo xoqo waxay sababtay inay bararaan oo cuncunayan 2 daqiiqo gudahood, laakiin astaamuhu way libdheen 15-20 daqiiqo gudahood (Darier's sign) .
A 6-year-old female, presented with multiple dark-colored lesions, which started over the scalp and further progressed to involve the face and trunk since past six months. She gave a history of elevation, redness, and itching on the lesions on application of pressure. There was no associated flushing, vomiting, diarrhoea, or wheeze. The personal and family history was not contributory. On examination, there were multiple hyperpigmented macules over the scalp, forehead, face, and neck in addition to minimally elevated hyperpigmented plaques over the chest and the back. Gentle rubbing of the lesions elicited urtication and itching within 2 min and it resolved within 15–20 minutes, suggestive of the Darier's sign.
A 6-year-old female, presented with multiple dark-colored lesions, which started over the scalp and further progressed to involve the face and trunk since past six months. She gave a history of elevation, redness, and itching on the lesions on application of pressure. There was no associated flushing, vomiting, diarrhoea, or wheeze. The personal and family history was not contributory. On examination, there were multiple hyperpigmented macules over the scalp, forehead, face, and neck in addition to minimally elevated hyperpigmented plaques over the chest and the back. Gentle rubbing of the lesions elicited urtication and itching within 2 min and it resolved within 15–20 minutes, suggestive of the Darier's sign.
