Lymphangioma - Limfangioma
Limfangioma (Lymphangioma) nyaéta malformasi sistem limfatik anu dicirikeun ku lesi anu kista témbok ipis. Malformasi ieu tiasa lumangsung dina sagala umur sareng tiasa ngalibetkeun bagian mana waé awak, tapi 90 % lumangsung dina murangkalih umurna kirang ti 2 taun sareng ngalibatkeun sirah sareng beuheung. Limfangioma biasana didiagnosis sateuacan kalahiran nganggo ultrasonografi fétal. Limfangioma akuisisi (Acquired lymphangioma) tiasa hasil tina trauma, peradangan, atanapi halangan limfatik. Kusabab aranjeunna henteu ngagaduhan kasempetan janten ganas, limfangioma biasana dirawat pikeun alesan kosmetik wungkul.
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ReferencesLymphangioma ogé katelah malformasi limfatik (LM). Ieu gangguan vaskular hadir ti lahir. Ieu dicirikeun ku tumuwuhna abnormal jaringan limfatik saméméh jeung sanggeus kalahiran. Lymphangioma mangaruhan kira‑kira 1 dina 2000 nepi ka 4000 jalma, tanpa béda anu signifikan antara génder atawa ras. Kaseueuran kasus (80‑90 %) didiagnosis sateuacan umur dua. Gejalana rupa‑rupa lega, ti bareuh lokal nepi ka abnormalitas éksténsif dina saluran limfatik, sakapeung ngabalukarkeun bareuh parna katelah elephantiasis. Contona, lymphangioma dina beuheung jeung beungeut bisa ngabalukarkeun bareuh raray, sarta dina kasus parna, disfigurement. Lamun mangaruhan létah, éta bisa ngakibatkeun rahang overgrowth (mandibular overgrowth) jeung huntu misaligned (occlusal asymmetry). Dina sungut sareng beuheung, éta tiasa nyababkeun masalah engapan (obstructive acute respiratory distress) sareng kaayaan darurat anu ngancam kahirupan (life‑threatening). Dina panon, éta bisa ngabalukarkeun leungitna visi (decreased vision), gerakan panon kawates (decreased extraocular muscle movement), drooping kongkolak panon (ptosis), sarta panon nonjol (exophthalmos). Keterlibatan anggota awak tiasa nyababkeun bareuh sareng pertumbuhan abnormal jaringan sareng tulang. Tumor ieu biasana tumuwuh lalaunan, tapi inféksi, parobahan hormonal, atawa tatu bisa ngabalukarkeun tumuwuhna gancang, posing resiko‑ngancam kahirupan anu merlukeun perlakuan urgent.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Dina ulikan retrospective ieu, urang marios 24 murangkalih anu ngagaduhan lymphangioma sareng dirawat kalayan suntikan solusi bleomycin ti Januari 1999 dugi ka Désémber 2004. Seuseueurna lesi (63%) parantos ngaleungit, 21% ngagaduhan réspon anu saé, sareng 16% teu ngabales alus. Dua pasien ngagaduhan tumor deui engké, sareng dua sanésna ngagaduhan bisul dimana aranjeunna nampi suntikan. Kabeneran, kami henteu ningali masalah ageung atanapi efek samping anu sanés.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
Jenis utama lymphangioma nyaéta kieu – lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Ieu nyababkeun sakitar 26 % tina tumor vaskular bénin di murangkalih tapi jarang di déwasa. Lymphangioma circumscriptum, tipe nu pangseringna, nembongkeun saluran limfatik nu nongol ngaliwatan kulit, ngabentuk vesikel nu jelas dieusi cairan sarupa spawn bangkong, babarengan jeung bareuh jaringan. Biasana kapanggih di daérah anu boga jaringan limfatik loba kawas anggota awak deukeut, batang, jeung aksila. Wanoja umur 71 taun sumping ka klinik kami kalayan bengkak suku nu terus‑terusan, kumpulan papul pink dina labia, gatal, jeung cairan limfa nu ngocor. Urang ngalakukeun labiektomi (labiectomy) mayor bilateral nepi ka tingkat fascia Colles, bari ngajaga klitoris jeung fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
