Lymphangioma - Limfangioma
Limfangioma (Lymphangioma) nyaéta malformasi sistem limfatik anu dicirikeun ku lesi kista kalayan témbok ipis. Malformasi ieu tiasa lumangsung dina sagala umur sareng tiasa ngalibetkeun bagian mana waé awak, tapi 90 % lumangsung dina murangkalih umurna kirang ti 2 taun sareng biasana ngalibetkeun sirah sareng beuheung. Limfangioma biasana didiagnosis sateuacan lahir ngagunakeun ultrasonografi fétal. Limfangioma akuisisi tiasa hasil tina trauma, peradangan, atanapi obstruksi limfatik. Kusabab teu boga potensi janten ganas, limfangioma biasana dirawat pikeun tujuan kosmetik wungkul.
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ReferencesLymphangioma ogé katelah malformasi limfatik (LM). Ieu gangguan vaskular hadir ti lahir. Ieu dicirikeun ku tumuwuhna jaringan limfatik anu abnormal saméméh jeung sanggeus kalahiran. Lymphangioma mangaruhan kira-kira 1 dina 2000 nepi ka 4000 jalma, tanpa bédana signifikan antara gender atawa ras. Kaseueuran kasus (80‑90 %) didiagnosis saméméh umur dua taun. Gejalana rupa-rupa, ti bengkak lokal nepi ka abnormalitas éksténsif dina saluran limfatik, sakapeung nyababkeun bengkak parna anu disebut elephantiasis. Contona, lymphangioma dina beuheung jeung beungeut bisa nyababkeun bengkak raray, sarta dina kasus parna, ngabalukarkeun deformitas. Lamun mangaruhan létah, éta bisa nyababkeun rahang overgrowth jeung huntu misaligned. Dina sungut jeung beuheung, éta tiasa nyababkeun gangguan napas jeung kaayaan darurat anu ngancam kahirupan. Dina panon, éta bisa ngabalukarkeun leungitna visi, gerakan panon kawates, drooping (kongkolak) panon, sarta panon nonjol. Keterlibatan anggota awak tiasa nyababkeun bengkak jeung pertumbuhan jaringan abnormal sarta tulang. Tumor ieu biasana tumuwuh lalaunan, tapi inféksi, parobahan hormonal, atawa tatu bisa ngabalukarkeun pertumbuhan gancang, nimbulkeun résiko anu ngancam kahirupan anu merlukeun perlakuan darurat.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Dina ulikan retrospektif ieu, urang marios 24 murangkalih anu ngagaduhan lymphangioma sareng dirawat ku suntikan solusi bleomycin ti Januari 1999 dugi ka Désémber 2004. Seuseueurna lesi (63 %) parantos ngaleungit, 21 % nunjukkeun réspon anu saé, sareng 16 % teu ngabales sacara signifikan. Dua pasien ngalaman tumor kambuh engké, sarta dua deui ngalaman bisul di tempat suntikan. Kabeneran, kami teu ningali masalah serius atawa efek samping séjén.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
Jenis utama lymphangioma nyaéta kieu: lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Ieu nyababkeun sakitar 26 % tina tumor vaskular bénign di murangkalih, tapi jarang kapanggih di déwasa. Lymphangioma circumscriptum, tipe nu pangseringna, nembongkeun saluran limfatik nu nongol ngaliwatan kulit, ngabentuk vesikel nu jelas dieusi cairan sarupa “spawn bangkong”, sarta dibarengan ku pembengkakan jaringan. Biasana muncul di daérah anu boga jaringan limfatik, sapertos anggota awak, batang, jeung kelek. Wanoja umur 71 taun sumping ka klinik kami kalayan bengkak suku nu terus-terusan, nyeri, gatal-gatal, sarta cairan limfa nu bocor. Urang bedah ngaleungitkeun sagala jaringan nu kapangaruhan ku prosedur anu disebut bilateral major labiectomy, nepi ka tingkat fascia Colles', bari ngajaga klitoris jeung fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
