Angiofibroma - Anjiyofibromahttps://en.wikipedia.org/wiki/Angiofibroma
Anjiyofibroma (Angiofibroma) - qattiq papula, tugun yoki o'simta lezyonlari. Angiofibromlar ba'zida akne sifatida noto'g'ri tashxis qo'yiladi. Ular joylashgan joyi bo'yicha shunday nomlanadi:
1) yuz
Fibrous papule
2) jinsiy olatni
Pearly penile papule
3) tirnoq yoki oyoq tirnoqlari ostida
Periungual angiofibroma
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  • Anjiyofibroma (Angiofibroma) akne kabi ko'rinishga ega. Lezyonlar asosan burun atrofida paydo bo'ladi.
    References Cutaneous Angiofibroma 29494077 
    NIH
    Cutaneous angiofibromas tananing turli qismlarida paydo bo'lishi mumkin. Yuzda ular ko'pincha tolali papulalar yoki sebaceum adenomasi sifatida tanilgan; jinsiy olatni ustida ular pearly penile papules deb ataladi; tirnoq ostida ular periungual angiofibromlar yoki Koenen o'smalari deb ataladi; og'izda esa ular og'iz fibromasi deb ataladi. Yuz angiofibromalari teri, buyraklar, yurak, miya va o'pkalarga ta'sir qiluvchi irsiy kasallik bo'lgan tuberous sclerosis (TS) ning muhim xususiyatidir. Ular odatda TS bilan og'rigan odamlarda bolalik yoki erta balog'at davrida yuzida rivojlanadi. Uch yoki undan ortiq yuz angiofibromasi yoki ikki yoki undan ortiq periungual angiofibromalari TS diagnostikasi uchun muhim hisoblanadi. Bundan tashqari, yuzning bir nechta angiofibromlari mavjud bo'lishi mumkin (multiple endocrine neoplasia type 1 (MEN-1) va Birt-Hogg-Dubé syndrome) . Pearly penile papules jinsiy olatni koronal chetida va bo'shlig'ida joylashgan. Ular ko'pincha sunnatsiz erkaklarda kuzatiladigan doimiy, og'riqsiz shishlardir.
    Cutaneous angiofibromas can be located on different areas of the body including the face where they are commonly called fibrous papules or adenoma sebaceum on the penis where they are called pearly penile papules, underneath the nail where they are called periungual angiofibromas or Koenen tumors, and in the mouth where they are called oral fibromas. Facial angiofibromas are considered one of the most obvious clinical presentations of tuberous sclerosis (TS), an autosomal dominant hamartomatous disorder that affects the skin, kidneys, heart, brain, and lungs. With TS, angiofibromas typically arise on the face in childhood and early adulthood. Both facial angiofibromas (greater than or equal to 3 needed) and periungual angiofibroma (greater than or equal to 2 needed) are 2 of the major criteria for TS. Multiple facial angiofibromas are also found in multiple endocrine neoplasia type 1 (MEN-1) and Birt-Hogg-Dube syndrome. Pearly penile papules are chronic, asymptomatic, papules found on the coronal margin and sulcus of the penis. They are more common in uncircumcised men.