Anjiyofibroma (Angiofibroma) – qattiq papula, tugun yoki o‘simta lezyonlari. Angiofibromlar ba‘zida akne sifatida noto‘g‘ri tashxis qo‘yiladi. Ular joylashgan joyiga ko‘ra quyidagicha nomlanadi: 1) yuz – Fibrous papule 2) jinsiy organ (penis) – Pearly penile papule 3) tirnoq yoki oyoq tirnoqlari ostida – Periungual angiofibroma
Angiofibromas are small, reddish brown or even flesh-colored, smooth, shiny, 0.1 to 0.3 cm papules present over the sides of the nose and the medial portions of the cheeks. They contain fibrous tissue.
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Anjiyofibroma (Angiofibroma) aknega o‘xshash ko‘rinishga ega. Lezyonlar asosan burun atrofida paydo bo‘ladi.
Cutaneous angiofibromalar tananing turli qismlarida paydo bo'lishi mumkin. Yuzda ular ko'pincha tolali papulalar yoki sebaceum adenomasi sifatida tanilgan; jinsiy olat ustida esa pearly penile papules deb ataladi; tirnoq ostida periungual angiofibromalar yoki Koenen o'smalari deb ataladi; og'izda esa og'iz fibromasi deb ataladi. Yuz angiofibromalari tuberous sclerosis (TS) – bu teri, buyraklar, yurak, miya va o'pkalarga ta'sir qiluvchi irsiy kasallikning muhim belgisi hisoblanadi. Ular odatda TS bilan og'rigan shaxslarda bolalik yoki erta balog'at davrida yuzda rivojlanadi. Uch yoki undan ortiq yuz angiofibromasi yoki ikki yoki undan ortiq periungual angiofibromalari TS diagnostikasi uchun muhim hisoblanadi. Bundan tashqari, yuzda bir nechta angiofibromalar (multiple endocrine neoplasia type 1 (MEN-1) va Birt-Hogg-Dubé syndrome) ham bo'lishi mumkin. Pearly penile papules jinsiy olatning koronal chetida va bo'shlig'ida joylashgan. Ular ko'pincha sunnatsiz erkaklarda kuzatiladigan doimiy, og'riqsiz shishlardir. Cutaneous angiofibromas can be located on different areas of the body including the face where they are commonly called fibrous papules or adenoma sebaceum on the penis where they are called pearly penile papules, underneath the nail where they are called periungual angiofibromas or Koenen tumors, and in the mouth where they are called oral fibromas. Facial angiofibromas are considered one of the most obvious clinical presentations of tuberous sclerosis (TS), an autosomal dominant hamartomatous disorder that affects the skin, kidneys, heart, brain, and lungs. With TS, angiofibromas typically arise on the face in childhood and early adulthood. Both facial angiofibromas (greater than or equal to 3 needed) and periungual angiofibroma (greater than or equal to 2 needed) are 2 of the major criteria for TS. Multiple facial angiofibromas are also found in multiple endocrine neoplasia type 1 (MEN-1) and Birt-Hogg-Dube syndrome. Pearly penile papules are chronic, asymptomatic, papules found on the coronal margin and sulcus of the penis. They are more common in uncircumcised men.
1) yuz – Fibrous papule
2) jinsiy organ (penis) – Pearly penile papule
3) tirnoq yoki oyoq tirnoqlari ostida – Periungual angiofibroma