Lymphangioma - Lenfangioma
Lenfangioma (Lymphangioma) - ingichka devorli kistalar bo'lgan lezyonlar bilan tavsiflangan limfa tizimining malformatsiyasi. Ushbu malformatsiyalar har qanday yoshda paydo bo'lishi mumkin va tananing har qanday qismini qamrab olishi mumkin, ammo 90% 2 yoshgacha bo'lgan bolalarda uchraydi va bosh va bo'yinni qamrab oladi. Limfangiomalar odatda homila ultratovush tekshiruvi yordamida tug'ilishdan oldin tashxis qilinadi. Olingan limfangiomalar travma, yallig'lanish yoki limfatik obstruktsiya natijasida paydo bo'lishi mumkin. Ularning malign bo'lish ehtimoli yo'qligi sababli, limfangioma odatda faqat kosmetik sabablarga ko'ra davolanadi.
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ReferencesLymphangioma limfa malformatsiyasi (LM) deb ham ataladi. Bu tug‘ilishdan beri mavjud bo‘lgan qon tomir kasalligi. Bu tug‘ilishdan oldin va keyin limfa to‘qimalarining anormal o‘sishi bilan tavsiflanadi. Lymphangioma har 2000‑4000 kishiga bir marta uchraydi, jins yoki irq o‘rtasida sezilarli farq yo‘q. Aksariyat hollarda (80‑90 %) ikki yoshdan oldin tashxis qo‘yiladi. Semptomlar keng tarqalgan bo‘lib, mahalliy shishishdan tortib limfa kanallarida keng tarqalgan anormalliklarga qadar, ba‘zan esa filioz (elephantiasis) deb ataladigan kuchli shishga olib keladi. Masalan, bo‘yin va yuzdagi lymphangioma yuzning shishishiga (facial elephantiasis), og‘ir holatlarda esa buzilishga (serious disfigurement) olib kelishi mumkin. Tilga ta’sir qilganda, bu jag‘ning haddan tashqari o‘sishiga (mandibular overgrowth) va tishlarning noto‘g‘ri joylashuviga (occlusal asymmetry) olib kelishi mumkin. Og‘iz va bo‘yin (oral and cervical) LM nafas olish yo‘llarini tiqib qo‘yishi (obstructive acute respiratory distress) va hayot uchun xavfli vaziyatlarga (life‑threatening situations) olib kelishi mumkin. Ko‘zlarda bu ko‘rishning yo‘qolishiga (decreased vision), ko‘z harakatining cheklanishiga (decreased extraocular muscle movement), ko‘z qovoqlarining tushishiga (ptosis) va ko‘zlarning shishishiga (exophthalmos) olib kelishi mumkin. Oyoq‑qo‘llarda bu shishish yoki gigantizmga (gigantism), yumshoq to‘qima va suyaklarning haddan tashqari o‘sishiga (overgrowth of soft tissue and bones) olib kelishi mumkin. Bu o‘simta odatda sekin o‘sib boradi, ammo infektsiyalar, gormonal o‘zgarishlar yoki shikastlanishlar tez o‘sishga olib kelishi mumkin, bu esa shoshilinch davolanishni talab qiladigan hayot uchun xavfli vaziyatga (life‑threatening condition) olib keladi.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Ushbu retrospektiv tadqiqotda biz 1999 yil yanvaridan 2004 yil dekabrigacha lymphangioma bo‘lgan va bleomycin eritmasi in‘ektsiyalari bilan davolangan 24 nafar bolani ko‘rib chiqdik. Ko‘pgina lezyonlar (lesions) (63%) butunlay yo‘qoldi, 21% yaxshi javob oldi va 16% yaxshi javob bermadi. Ikki bemorda tumor (tumour) keyinroq qaytgan, yana ikkitasida esa in‘ektsiya qilingan joyda abscess bor. Yaxshiyamki, biz boshqa katta muammolar yoki nojo‘ya ta’sirlarni ko‘rdik.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
Lymphangioma ning asosiy turlari quyidagilardir - lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Ular bolalardagi qon tomir o‘smalarining 26% ni tashkil qiladi, lekin kattalarda kamroq uchraydi. Lymphangioma circumscriptum, eng tez-tez uchraydigan turi, teri bo‘ylab chiqadigan limfa yo‘llarini ko‘rsatadi, to‘qimalarning shishishi bilan birga qurbaqa urug‘iga o‘xshash shaffof suyuqlik bilan to‘ldirilgan pufakchalarni hosil qiladi. Odatda oyoq‑qo‘llar, torso (trunk) va qo‘ltiqlar kabi boy limfa tarmog‘iga ega bo‘lgan joylarda paydo bo‘ladi. Klinikamizga 71 yoshli ayol oyoqlarining doimiy shishishi, jinsiy a’zolarida pushti dog‘lar, qichishish, limfa suyuqligining oqishi bilan keldi. Biz jarrohlik yo‘li bilan ikki tomonlama katta labiektomiya deb ataladigan operatsiya bilan barcha shishlarni olib tashladik, Kolles fasyasi darajasida to‘xtab, klitoris va to‘rtshetni saqlab qoldik.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
