Angiofibroma - I-Angiofibroma
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References
Cutaneous angiofibromas inokuvela kwiindawo ezahlukeneyo zomzimba. Ebusweni, zidla ngokuziwa ngokuba ziifibrous papules okanye i-adenoma sebaceum; kwilungu lobudoda, babizwa pearly penile papules ; ngaphantsi kwesikhonkwane, zibizwa ngokuba zii-periungual angiofibromas okanye i-Koenen tumors; kwaye emlonyeni, zibizwa ngokuba zii-fibromas zomlomo. I-angiofibromas yobuso luphawu olubalaseleyo lwe- tuberous sclerosis (TS) , ingxaki efunyenwe njengelifa echaphazela ulusu, izintso, intliziyo, ingqondo, kunye nemiphunga. Ngokuqhelekileyo bakhula ebusweni ngexesha lobuntwana okanye ebuntwini obukhulu kubantu abane-TS. Ukuba ne-angiofibromas yobuso ezintathu okanye ngaphezulu okanye ezimbini okanye ngaphezulu ze-periungual angiofibromas zithathwa ngokuba zibalulekile ekuxilongeni i-TS. Ukongeza, i-angiofibromas yobuso emininzi inokubakho kwiimeko (multiple endocrine neoplasia type 1 (MEN-1) kunye Birt-Hogg-Dubé syndrome) . Pearly penile papules zifumaneka ecaleni komda we-coronal kunye ne-sulcus yelungu lobudoda. Ngamaqhuma azingisayo, angenabuhlungu abonwa kakhulu kumadoda angolukanga.
Cutaneous angiofibromas can be located on different areas of the body including the face where they are commonly called fibrous papules or adenoma sebaceum on the penis where they are called pearly penile papules, underneath the nail where they are called periungual angiofibromas or Koenen tumors, and in the mouth where they are called oral fibromas. Facial angiofibromas are considered one of the most obvious clinical presentations of tuberous sclerosis (TS), an autosomal dominant hamartomatous disorder that affects the skin, kidneys, heart, brain, and lungs. With TS, angiofibromas typically arise on the face in childhood and early adulthood. Both facial angiofibromas (greater than or equal to 3 needed) and periungual angiofibroma (greater than or equal to 2 needed) are 2 of the major criteria for TS. Multiple facial angiofibromas are also found in multiple endocrine neoplasia type 1 (MEN-1) and Birt-Hogg-Dube syndrome. Pearly penile papules are chronic, asymptomatic, papules found on the coronal margin and sulcus of the penis. They are more common in uncircumcised men.
Cutaneous angiofibromas can be located on different areas of the body including the face where they are commonly called fibrous papules or adenoma sebaceum on the penis where they are called pearly penile papules, underneath the nail where they are called periungual angiofibromas or Koenen tumors, and in the mouth where they are called oral fibromas. Facial angiofibromas are considered one of the most obvious clinical presentations of tuberous sclerosis (TS), an autosomal dominant hamartomatous disorder that affects the skin, kidneys, heart, brain, and lungs. With TS, angiofibromas typically arise on the face in childhood and early adulthood. Both facial angiofibromas (greater than or equal to 3 needed) and periungual angiofibroma (greater than or equal to 2 needed) are 2 of the major criteria for TS. Multiple facial angiofibromas are also found in multiple endocrine neoplasia type 1 (MEN-1) and Birt-Hogg-Dube syndrome. Pearly penile papules are chronic, asymptomatic, papules found on the coronal margin and sulcus of the penis. They are more common in uncircumcised men.
1) ubuso
Fibrous papule
2) incanca
Pearly penile papule
3) ngaphantsi kweminwe okanye inzwane
Periungual angiofibroma