Lymphangioma
Lymphangioma zizinto ezigwenxa ze-lymphatic system eziphawulwa ngamanxeba angama-cysts abhityileyo. Ezi mpazamo zingenzeka nanini na ubudala kwaye zingabandakanya nayiphi na inxalenye yomzimba, kodwa i-90% yenzeke kubantwana abangaphantsi kweminyaka engama-2 ubudala kwaye ibandakanya intloko nentamo.I-Lymphangiomas ifunyanwe ngokuqhelekileyo ngaphambi kokuzalwa isebenzisa i-fetal ultrasonography. I-lymphangiomas efunyenweyo inokubangelwa kukwenzakala, ukudumba, okanye ukuvaleka kwe-lymphatic. Ekubeni bengenalo ithuba lokuba yingozi, i-lymphangiomas idla ngokunyangwa ngenxa yezizathu zokuthambisa kuphela.
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References
Lymphangioma ikwabizwa ngokuba yi-lymphatic malformation (LM) . Sisifo semithambo ekhoyo ukususela ekuzalweni. Ibonakala ngokukhula okungaqhelekanga kwezicubu ze-lymphatic ngaphambi nasemva kokuzalwa. Lymphangioma ichaphazela malunga nomntu omnye ngo-2000 ukuya kuma-4000 abantu, kungekho mahluko ubalulekileyo phakathi kwesini okanye iintlanga. Uninzi lweziganeko (80-90%) zifunyaniswa ngaphambi kweminyaka emibini. Iimpawu ziyahluka ngokubanzi, ukusuka ekudumbeni kwendawo ukuya kwizinto ezingaqhelekanga kwimijelo ye-lymphatic, ngamanye amaxesha okukhokelela ekudumbeni okukhulu okubizwa ngokuba yi-elephantiasis. Umzekelo, lymphangioma entanyeni nasebusweni kunokubangela ukudumba kobuso, kwaye kwiimeko ezinzima, ukonakala. Xa ichaphazela ulwimi, inokukhokelela ekukhuleni kwemihlathi kunye namazinyo angahambelani kakuhle. Emlonyeni nasentanyeni, kunokubangela iingxaki zokuphefumla kunye neemeko ezisongela ubomi. Emehlweni, kunokubangela ukulahleka kombono, ukungahambi kakuhle kwamehlo, ukugoba iinkophe, kunye namehlo adumbileyo. Ukubandakanyeka kwelungu kunokubangela ukudumba kunye nokukhula okungaqhelekanga kwezicubu kunye namathambo. Eli thumba ngokuqhelekileyo likhula ngokukhawuleza, kodwa izifo, utshintsho lwe-hormonal, okanye ukulimala kunokubangela ukukhula ngokukhawuleza, ukubeka imingcipheko esongela ubomi efuna unyango oluphuthumayo.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Kolu phononongo lokubuyela umva, saphonononga abantwana abangama-24 ababene lymphangioma kwaye banyangwa ngeenaliti zesisombululo sebleomycin ukusuka ngoJanuwari 1999 ukuya kuDisemba 2004. Uninzi lwezilonda (63%) zahamba ngokupheleleyo, i-21% yafumana impendulo entle, kunye ne-16% khange aphendule kakuhle. Izigulana ezibini ziye zabuya emva kwexesha, kwaye abanye ababini bafumana amathumba apho bafumana khona iinaliti. Ngethamsanqa, asizange sibone ezinye iingxaki ezinkulu okanye iziphumo ebezingalindelekanga.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
Iindidi eziphambili ze lymphangioma zezi zilandelayo - lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Ezi zenza malunga ne-26% ye-benign vascular tumors ebantwaneni kodwa ayixhaphakanga kakhulu kubantu abadala. Lymphangioma circumscriptum , olona hlobo luxhaphakileyo, lubonisa imibhobho ye-lymphatic ephuma esikhumbeni, yenze i-vesicles ecacileyo ezaliswe lulwelo efana nokuzala kwesele, kunye nokudumba kwethishu. Ngokuqhelekileyo ibonakala kwiindawo ezinothungelwano olutyebileyo lwe-lymphatic efana nemilenze, i-trunk, kunye ne-armpits. Ixhegwazana elineminyaka engama-71 ubudala leza kwikliniki yethu lidumba okuthe gqolo ukudumba, amaqhuma apinki kumalungu akhe angasese, ukurhawuzelelwa, kunye nolwelo lwe-lymph oluvuzayo. Sasusa ngotyando onke amaqhuma ngenkqubo ebizwa ngokuba yi-bilateral major labiectomy, simisa kwinqanaba le-Colles' fascia, ngelixa sigcina iclitoris kunye ne-fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
