Neurofibromatosis jẹ àìlera àtọkànwá ti ara ẹni tí ó ń ṣẹlẹ̀ nípasẹ̀ àyípadà nínú neurofibromin. Neurofibromatosis ń fa àwọn àìlera pẹ̀lú eto aifọkanbalẹ, tí ó lè dàgbà ní ibikíbi lórí ara. Ó jẹ́ ọ̀kan nínú àwọn àìlera jiini tí ó wọ́pọ̀ jùlọ, tí ó sì ní àkúnya autosomal.
Àwọn ààmì àìlera tó wọ́pọ̀ jùlọ ti neurofibromatosis ni àwọn ààyè pupa dídá tí ó dà bí brownish‑pupa lórí awọ oju, tí a ń pè ní Lisch nodules àti neurofibromas. Scoliosis (ìsépo ti ọpa ẹhin), àìlera ìkèkọ́, àìlera ojúran, àìlera ọpọlọ, ọ̀pọ̀ café au lait spots, àti warapa lè wà pẹ̀lú.
Neurofibromatosis type I (NF-1) is a complex multi-system human disorder caused by the mutation of a gene on chromosome 17 that is responsible for production of a protein, called neurofibromin, which is needed for normal function in many human cell types.
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Café au lait macule ti a ri ninu Neurofibromatosis type 1 (NF-1)
Neurofibromatosis jẹ ipo kan ti o fa awọn èèmọ ninu eto aifọkanbalẹ ati awọ ara. Iru 1 jẹ ti a jogun, o sì ṣafihan awọn ami aisan bii neurofibromas, café‑au‑lait spots, freckling, àti optic gliomas. Ayẹwo aisan da lori awọn ami aisan. Iru 2, ní apa keji, ti samisi nipasẹ bilateral vestibular schwannomas (VS) àti meningiomas, tí a tún le jogun. Isakoso pẹ̀lú abojuto deede àti itọju ilera gẹ́gẹ́ bí a ṣe nílò fún àwọn oríṣi méjèèjì ti neurofibromatosis. Neurofibromatosis is a neurocutaneous disorder characterized by tumors in the nervous system and skin. Neurofibromatosis types 1 and 2 are the most common and are distinct entities. Neurofibromatosis type 1, or von Recklinghausen disease, is an autosomal dominant disease. Neurofibromatosis type 1 presents with neurofibromas, cafe-au-lait macules, freckling, and optic gliomas. It is a clinical diagnosis. Neurofibromatosis type 2 (NF2) is a disease characterized by bilateral vestibular schwannomas (VS) and meningiomas. It has an autosomal dominant inheritance pattern. Treatment for neurofibromatosis types 1 and 2 is clinical monitoring and medical intervention when appropriate.
Àwọn ààmì àìlera tó wọ́pọ̀ jùlọ ti neurofibromatosis ni àwọn ààyè pupa dídá tí ó dà bí brownish‑pupa lórí awọ oju, tí a ń pè ní Lisch nodules àti neurofibromas. Scoliosis (ìsépo ti ọpa ẹhin), àìlera ìkèkọ́, àìlera ojúran, àìlera ọpọlọ, ọ̀pọ̀ café au lait spots, àti warapa lè wà pẹ̀lú.
Kò sí ìtọ́jú pàtó títí di báyìí.