Lymphangioma - I-Lymphangioma
I-Lymphangioma (Lymphangioma) kuwukonakala kwesistimu ye-lymphatic ebonakala ngamanxeba angama-cysts anezindonga ezincane. Lezi zinkinga zingenzeka kunoma ibuphi ubudala futhi zingase zihilele noma iyiphi ingxenye yomzimba, kodwa u-90% zenzeka ezinganeni ezingaphansi kweminyaka engu-2 ubudala futhi zihlanganisa ikhanda nentamo.I-Lymphangiomas ivame ukutholakala ngaphambi kokuzalwa kusetshenziswa i-fetus ultrasonography. I-lymphangiomas etholiwe ingase ibangele ukuhlukumezeka, ukuvuvukala, noma ukuvinjelwa kwe-lymphatic. Njengoba bengenalo ithuba lokuba yingozi, i-lymphangiomas ivame ukwelashwa ngezizathu zezimonyo kuphela.
☆ Emiphumeleni ka-2022 ye-Stiftung Warentest evela eJalimane, ukwaneliseka kwabathengi nge-ModelDerm bekungaphansi kancane kunokuxhumana okukhokhelwayo kwe-telemedicine.
References
Lymphangioma yaziwa nangokuthi i-lymphatic malformation (LM) . Kuwukuphazamiseka kwemithambo ekhona kusukela ekuzalweni. Kubonakala ngokukhula okungavamile kwezicubu ze-lymphatic ngaphambi nangemuva kokuzalwa. Lymphangioma ithinta cishe oyedwa ngo-2000 kuya kubantu abangu-4000, kungekho mehluko omkhulu phakathi kobulili noma izinhlanga. Izimo eziningi (80-90%) zitholwa ngaphambi kweminyaka emibili. Izimpawu ziyahlukahluka kakhulu, kusukela ekuvuvukeni kwendawo kuye kokungajwayelekile okuningi emiseleni ye-lymphatic, kwesinye isikhathi okuholela ekuvuvukeni okukhulu okwaziwa nge-elephantiasis. Isibonelo, i- lymphangioma entanyeni nasebusweni ingabangela ukuvuvukala kobuso, futhi ezimeni ezinzima, ukonakala. Uma ithinta ulimi, ingaholela ekukhuleni kwemihlathi kanye namazinyo angahambi kahle. Emlonyeni nasentanyeni, kungabangela izinkinga zokuphefumula kanye nezimo eziphuthumayo ezisongela ukuphila. Emehlweni, kungase kubangele ukulahlekelwa ukubona, ukunyakaza kwamehlo okulinganiselwe, amajwabu amehlo alengele, namehlo aqhumile. Ukubandakanyeka kwezitho kungabangela ukuvuvukala nokukhula okungavamile kwezicubu namathambo. Lesi simila ngokuvamile sikhula kancane, kodwa izifo, izinguquko zamahomoni, noma ukulimala kungabangela ukukhula ngokushesha, kubangele izingozi ezisongela ukuphila ezidinga ukwelashwa okuphuthumayo.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Lymphangioma (lymphatic malformation, LM), a congenital vascular disease, is a low-flow vascular abnormality in lymphatic diseases that is characterized by excessive growth of lymphatic tissue during prenatal and postpartum development. The incidence rate of LM is ~1:2000–4000, with no variation between genders and races. Most patients (80–90%) are diagnosed before the age of two. The clinical manifestations of lymphangioma are quite different among patients, varying from local swelling leading to superficial mass to a large area of diffuse infiltrating lymphatic channel abnormalities resulting in elephantiasis. Cervicofacial LM can cause facial elephantiasis, and in some severe cases, it can lead to serious disfigurement of the face. Tongue LM can lead to mandibular overgrowth and occlusal asymmetry, and oral and cervical LM can cause obstructive acute respiratory distress and life-threatening situations. Orbital LM may lead to decreased vision, decreased extraocular muscle movement, ptosis and exophthalmos. LM of the extremities can trigger swelling or gigantism, accompanied by overgrowth of soft tissue and bones. LM usually grows slowly and steadily, but under certain conditions, such as infection, hormonal changes or trauma, it can grow explosively and become a life-threatening disease requiring immediate treatment.
Kulolu cwaningo lokubheka emuva, sibuyekeze izingane ezingu-24 ezazine- lymphangioma futhi zalashwa ngemijovo yesisombululo se-bleomycin kusukela ngoJanuwari 1999 kuya kuDisemba 2004. Izilonda eziningi (63%) zaphela nya, u-21% wathola impendulo enhle, futhi u-16% akaphendulanga kahle. Iziguli ezimbili zathola isimila kamuva, kanti ezinye ezimbili zaqhuma amathumba lapho zathola khona imijovo. Ngenhlanhla, asizange sibone ezinye izinkinga ezinkulu noma imiphumela emibi.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
This is a retrospective study of 24 children diagnosed with lymphangioma and treated with intralesional injection of bleomycin aqueous solution from January 1999 to December 2004. Complete resolution was seen in 63% (15/24) of lesions, 21% (5/24) had good response and 16% (4/24) had poor response. The tumour recurred in 2 patients. Two other patients had abscess formation at the site of injection. No other serious complications or side effects were observed.
Izinhlobo eziyinhloko ze- lymphangioma zimi kanje - lymphangioma circumscriptum, cavernous lymphangioma, cystic hygroma, lymphangioendothelioma. Lezi zenza cishe u-26% wezimila ze-benign vascular ezinganeni kodwa azivamile kubantu abadala. I- lymphangioma circumscriptum , uhlobo oluvame kakhulu, lubonisa imigudu ye-lymphatic ephumela esikhumbeni, enza ama-vesicle agcwele uketshezi afana nokuzala kwesele, kanye nokuvuvukala kwezicubu. Ivamise ukuvela ezindaweni ezinenethiwekhi ye-lymphatic ecebile njengezitho, isiqu, namakhwapha. Owesifazane oneminyaka engu-71 weza emtholampilo wethu evuvuka njalo emlenzeni, enamaqhubu apinki esithweni sakhe sangasese, ukulunywa, noketshezi lwe-lymph oluvuzayo. Sasusa wonke amaqhubu ngokuhlinzwa ngenqubo ebizwa ngokuthi i-bilateral major labiectomy, sima ezingeni lika-Colles' fascia, kuyilapho silondoloza i-clitoris ne-fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
The predominant types of lymphangioma are lymphangioma circumscriptum (LC), cavernous lymphangioma, cystic hygroma, and lymphangioendothelioma. These entities account for approximately 26% of benign vascular tumors in children but are rarer in adults. LC is the most common form of cutaneous lymphangioma and is characterized by superficial lymphatic ducts protruding through the epidermis. This condition results in clusters of clear fluid-filled vesicles resembling frog spawn and associated tissue edema. It is usually found on the proximal extremity, trunk, and axilla, which has an abundant lymphatic system. A 71-year-old female presented to our outpatient clinic with persistent edema of both lower limbs, clusters of pink labial papules, pruritus, and watery lymph oozing. We removed all the papules by performing bilateral major labiectomy down to the level of Colles' fascia, sparing the clitoris and fourchette.
